Department of Otorhinolaryngology-Head and Neck Surgery, University Medical Center Utrecht, Heidelberglaan 100, PO Box 85500, 3508, GA, Utrecht, the Netherlands; UMC Utrecht Brain Center, Heidelberglaan 100, PO Box 85500, 3508, GA, Utrecht, the Netherlands.
Department of Otorhinolaryngology-Head and Neck Surgery, University Medical Center Utrecht, Heidelberglaan 100, PO Box 85500, 3508, GA, Utrecht, the Netherlands.
Int J Pediatr Otorhinolaryngol. 2021 Mar;142:110590. doi: 10.1016/j.ijporl.2020.110590. Epub 2020 Dec 22.
While research has shown that children with single sided deafness have a lower quality of life and developmental outcomes compared to normal hearing peers, little is known about these domains in children with unilateral congenital conductive hearing loss due to aural atresia.
This study aims to investigate the hearing-related quality of life, developmental outcomes and educational performance in children and young adults with unilateral conductive hearing loss due to aural atresia.
Nineteen children and young adults with unilateral aural atresia received a set of five questionnaires. Hearing-related quality of life (SSQ), general quality of life (Kidscreen-27), speech and language development (CCC-2-Nl), educational performance and problems in social-emotional and behavioral domains (CBCL/YSR/ASR) were measured with validated questionnaires. Scores on the questionnaires were compared to their norm scores. Mann-Whitney U tests and independent t-tests were used to identify significant differences between age groups.
Mean scores on the SSQ subscales were speech 6.78, spatial 5.00 and quality 6.98. Mean scores on the Kidscreen-27, CCC-2-NL, CBCL/YSR/ASR fell within normal or non-clinical range. A high number of cases needed speech therapy (60.7%) or special measures in class (79.3%) or showed grade repetition (>30%) in primary or secondary school.
Children and young adults with unilateral conductive hearing loss due to congenital aural atresia showed lower scores regarding hearing-related quality of life compared to normal-hearing peers. The result show similarities with children with single sided deafness. Regarding general quality of life, speech and language development and in social-emotional and behavioral domains the studied children and young adults seem to develop according to norm scores. It is important to observe these children closely as they may need guidance during education to allow them to thrive.
虽然研究表明，与正常听力的同龄人相比，单侧耳聋儿童的生活质量和发育结果较低，但由于先天性外耳闭锁导致单侧先天性传导性听力损失的儿童在这些领域的情况却知之甚少。
本研究旨在调查单侧先天性传导性听力损失儿童的听力相关生活质量、发育结果和教育表现。
19 名单侧外耳闭锁的儿童和年轻人接受了一套五份问卷。使用经过验证的问卷测量了听力相关生活质量（SSQ）、一般生活质量（Kidscreen-27）、言语和语言发展（CCC-2-Nl）、教育表现以及社会情感和行为领域的问题（CBCL/YSR/ASR）。将问卷得分与他们的常模得分进行比较。使用 Mann-Whitney U 检验和独立 t 检验来确定年龄组之间的显著差异。
SSQ 子量表的平均得分分别为言语 6.78、空间 5.00 和质量 6.98。Kidscreen-27、CCC-2-Nl、CBCL/YSR/ASR 的平均得分均处于正常或非临床范围内。有相当多的病例需要言语治疗（60.7%）或特殊课堂措施（79.3%），或在小学或中学阶段成绩重复（>30%）。
与正常听力的同龄人相比，先天性外耳闭锁导致单侧传导性听力损失的儿童和年轻人的听力相关生活质量得分较低。结果与单侧耳聋儿童相似。关于一般生活质量、言语和语言发展以及社会情感和行为领域，所研究的儿童和年轻人似乎按照常模得分发展。重要的是要密切观察这些儿童，因为他们在教育过程中可能需要指导，以帮助他们茁壮成长。
