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一名法洛四联症成年患者病例。

An Adult Patient With a Tetralogy of Fallot Case.

作者信息

Alkashkari Wail, Al-Husayni Faisal, Almaqati Ahmed, AlRahimi Jamilah, Albugami Saad

机构信息

Cardiology, King Abdullah International Medical Research Center, King Saud bin Abdulaziz University for Health Sciences, Jeddah, SAU.

Cardiology, King Faisal Cardiac Center, King Abdulaziz Medical City, Ministry of National Guard Health Affairs, Jeddah, SAU.

出版信息

Cureus. 2020 Nov 23;12(11):e11658. doi: 10.7759/cureus.11658.

DOI:10.7759/cureus.11658
PMID:33391897
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7769492/
Abstract

Tetralogy of Fallot (ToF) is considered the most frequent cyanotic congenital heart abnormality with a low adulthood survival rate if kept untreated. The majority of cases are symptomatic during infancy and mandate early treatment. Few instances of survival to asymptomatic middle-age patients have been reported, and they are decreasing due to early detection. We reported a case of a middle-aged man who was asymptomatic during his life and recently diagnosed with ToF. The patient underwent surgical repair with excellent outcomes. The case represents the possibility of diagnosing such cases in a relatively old patient despite medical development and advances.

摘要

法洛四联症(ToF)被认为是最常见的青紫型先天性心脏异常,如果不治疗,成年后的生存率较低。大多数病例在婴儿期出现症状,需要早期治疗。仅有少数存活至无症状中年患者的病例报道,且由于早期检测,这类病例正在减少。我们报告了一例中年男性病例,该患者一生中无症状,最近被诊断为法洛四联症。患者接受了手术修复,效果良好。该病例表明,尽管医学有所发展和进步,但仍有可能在相对年长的患者中诊断出此类病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/e69709d2e0de/cureus-0012-00000011658-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/c68455666c79/cureus-0012-00000011658-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/f7aaa9376152/cureus-0012-00000011658-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/81bcb6257bfe/cureus-0012-00000011658-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/e69709d2e0de/cureus-0012-00000011658-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/c68455666c79/cureus-0012-00000011658-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/f7aaa9376152/cureus-0012-00000011658-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/81bcb6257bfe/cureus-0012-00000011658-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff3d/7769492/e69709d2e0de/cureus-0012-00000011658-i04.jpg

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2
Quality of life in adults with repaired tetralogy of Fallot.法洛四联症修复术后成人的生活质量。
Kardiochir Torakochirurgia Pol. 2018 Jun;15(2):107-113. doi: 10.5114/kitp.2018.76476. Epub 2018 Jun 25.
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Tetralogy of Fallot in men: quality of life, family, education, and employment.男性法洛四联症:生活质量、家庭、教育与就业
成人法洛四联症未矫正的管理:一项叙述性综述。
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