Higashihara E, Munakata A, Hara M, Kitamura T, Kawabe K, Niijima T
Department of Urology, University of Tokyo, Japan.
Urology. 1988 Feb;31(2):155-8. doi: 10.1016/0090-4295(88)90044-1.
Medullary sponge kidney (MSK), parathyroid adenoma, renal cell carcinoma, and renal-leak hypercalciuria coincided in 1 female patient. Renal-leak hypercalciuria was not corrected by removal of a parathyroid adenoma. Since the patient had renal tubular acidosis (RTA), alkali treatment was conducted and resulted in the correction of hypercalciuria. Renal cell carcinoma eventually developed and MSK was confirmed histologically. This case suggests that MSK and primary hyperparathyroidism occurred independently.
1例女性患者同时患有髓质海绵肾(MSK)、甲状旁腺腺瘤、肾细胞癌和肾性漏钙性高钙尿症。切除甲状旁腺腺瘤后,肾性漏钙性高钙尿症并未得到纠正。由于该患者患有肾小管酸中毒(RTA),因此进行了碱治疗,结果高钙尿症得到纠正。最终发展为肾细胞癌,并经组织学证实为MSK。该病例提示MSK和原发性甲状旁腺功能亢进是独立发生的。