Reyniers Pieter, Wafa Hazem, Sinnaeve Friedl, Debeer Philippe, Sciot Raf
University Hospitals Leuven Campus Gasthuisberg, Herestraat 49, 3000 Leuven, Belgium.
SICOT J. 2021;7:2. doi: 10.1051/sicotj/2020048. Epub 2021 Jan 8.
Intraosseous schwannomas represent an extremely rare subgroup of schwannomas, accounting for <1% of all primary bone tumors. They mostly occur in the mandible, the maxilla, the sacrum, and they are also seen in long bones. We herein report a rare presentation of an intraosseous schwannoma in the glenoid of a 49-year-old patient. She complained of shoulder pain and was referred to the orthopaedic oncologist after detection of a suspicious lesion on imaging. Biopsy revealed benign spindle cells and immunohistochemistry was positive for S100. Because of the rarity of these intraosseous schwannomas it is important to recognize their radiological and histological features and make a differential diagnosis with other lytic tumors. Only if these characteristics are recognized, correct treatment can be given with definite curettage and bone grafting and correct follow-up with avoidance of unnecessary adjuvant therapy.
骨内神经鞘瘤是神经鞘瘤中极为罕见的一个亚组，占所有原发性骨肿瘤的比例不到1%。它们大多发生在下颌骨、上颌骨、骶骨，也可见于长骨。我们在此报告一例罕见的49岁患者肩胛盂骨内神经鞘瘤病例。她主诉肩部疼痛，影像学检查发现可疑病变后转诊至骨肿瘤专科医生处。活检显示为良性梭形细胞，免疫组化S100呈阳性。由于这些骨内神经鞘瘤罕见，认识其放射学和组织学特征并与其他溶骨性肿瘤进行鉴别诊断很重要。只有认识到这些特征，才能通过明确的刮除术和骨移植进行正确治疗，并进行正确的随访，避免不必要的辅助治疗。
