Rheumatology, VU University Medical Center, Amsterdam, The Netherlands.
Rheumatology, Reade, Amsterdam, The Netherlands.
BMJ Case Rep. 2021 Jan 15;14(1):e237549. doi: 10.1136/bcr-2020-237549.
We present a 51-year-old Caucasian woman, with a medical history of systemic lupus erythematosus (SLE) who had dyspnoea at exertion. The SLE was clinically quiescent but serologically active. Echocardiography showed preserved left ventricular (LV) systolic function, pseudonormal mitral inflow pattern (diastolic dysfunction grade III), absence of wall motion abnormalities and elevated E/e' at exercise. An exercise right heart catheterisation was performed, confirming the diagnosis of heart failure with preserved ejection fraction (HFpEF). In the absence of other possible causes, we assumed that HFpEF was mediated by systemic inflammation secondary to SLE. Based on the Paulus' paradigm, that systemic inflammation may lead to diastolic dysfunction, we decided to add belimumab (a biological agent against soluble B-lymphocyte stimulator protein). After 16 weeks of treatment, patient reported an improved condition. Also, cardiopulmonary exercise test and echocardiography results improved, confirming resolution of the underlying LV diastolic dysfunction. This case supports the idea that targeting inflammation has therapeutic potential in a subset of HFpEF-patients.
我们报告了一位 51 岁的白人女性,有系统性红斑狼疮 (SLE) 的病史,活动时呼吸困难。SLE 临床上处于静止期,但血清学上仍活跃。超声心动图显示左心室 (LV) 收缩功能正常,但二尖瓣口血流呈假性正常模式(舒张功能障碍 3 级),无壁运动异常,运动时 E/e'升高。进行了运动右心导管检查,确诊为射血分数保留的心力衰竭 (HFpEF)。由于没有其他可能的原因,我们假设 HFpEF 是由 SLE 引起的全身炎症介导的。根据 Paulus 的观点,全身炎症可能导致舒张功能障碍,我们决定加用贝利尤单抗(一种针对可溶性 B 淋巴细胞刺激蛋白的生物制剂)。治疗 16 周后,患者报告病情改善。心肺运动试验和超声心动图结果也有所改善,证实潜在的 LV 舒张功能障碍得到解决。这一病例支持了这样一种观点,即针对炎症可能对一部分 HFpEF 患者具有治疗潜力。