Gomes Fernanda, Melo Daniel, Esteves Cátia, Lima Beatriz, Carneiro Fátima, Oliveira Pedro
Radiology Department, Hospital de Braga, Sete Fontes - São Victor, 4710-243 Braga, Portugal.
Pathology Department, Centro Hospitalar de São João, Alameda Prof. Hernâni Monteiro, 4200-319 Porto, Portugal.
Radiol Case Rep. 2021 Jan 7;16(3):646-650. doi: 10.1016/j.radcr.2020.12.017. eCollection 2021 Mar.
The undifferentiated embryonal sarcoma of the liver is a rare tumor with a poor prognosis, with improved outcomes being reported with more recently multimodality treatments. We report a case of a 6-year-old girl with an incidentally diagnosed and histologically proven localized undifferentiated embryonal sarcoma of the liver. The divergence between solid appearance at US and cystic-like appearance on CT/MRI, which has been attributed to the presence of myxoid component frequently described with this tumor, was crucial for the diagnosis and subsequent treatment.
肝未分化胚胎性肉瘤是一种罕见肿瘤,预后较差,近期多模式治疗报告显示预后有所改善。我们报告一例6岁女孩,偶然诊断并经组织学证实为局限性肝未分化胚胎性肉瘤。超声检查显示的实性表现与CT/MRI上类似囊肿的表现之间的差异,归因于该肿瘤常有的黏液样成分,这对诊断及后续治疗至关重要。