Ibrahimi Ahmed, Hosni Abdelmoughit, Ziani Idriss, Laamrani Fatima Zahra, El Sayegh Hachem, Jroundi Laila, Benslimane Lounis, Nouini Yassine
Department of Urology A, Ibn Sina University Hospital, Rabat, Morocco.
Faculty of Medicine and Pharmacy, Mohammed V University in Rabat, Morocco.
Case Rep Urol. 2020 Dec 9;2020:8826664. doi: 10.1155/2020/8826664. eCollection 2020.
Zinner's syndrome is a rare congenital malformation of the seminal vesicle and ipsilateral upper urinary tract, due to developmental arrest in early embryogenesis of the Müllerian duct. Clinical presentation is nonspecific and includes voiding symptoms such as dysuria, ejaculatory disorders, and hypogastric or perineal pain. The diagnosis is made with imaging techniques, notably Magnetic Resonance Imaging (MRI) which remains the gold standard exam for diagnosis confirmation and therapeutic management. Treatment options depend on the severity of symptoms, the size of the cyst, and the complications. Herein, we report a rare case of a 33-year-old young patient who presented recurrent dysuria and ejaculatory disorders for the last 5 years. Imaging studies revealed an empty left renal fossa, with cystic pelvic mass related to the seminal vesicle and which was compatible with the diagnosis of Zinner's syndrome. The patient underwent successful laparoscopic removal of the cyst and seminal vesicle, with total disappearance of urinary and sexual complaints with a 3-year follow-up.
齐纳综合征是一种罕见的精囊和同侧上尿路先天性畸形，由于苗勒管早期胚胎发育停滞所致。临床表现不具特异性，包括排尿症状如排尿困难、射精障碍以及下腹部或会阴疼痛。诊断通过影像学技术进行，尤其是磁共振成像（MRI），它仍是确诊和治疗管理的金标准检查。治疗方案取决于症状的严重程度、囊肿大小及并发症。在此，我们报告一例罕见病例，一名33岁年轻患者在过去5年中反复出现排尿困难和射精障碍。影像学检查显示左肾窝空虚，盆腔有与精囊相关的囊性肿块，符合齐纳综合征的诊断。患者接受了成功的腹腔镜下囊肿及精囊切除术，随访3年，泌尿及性方面的不适完全消失。
