Svetanoff Wendy Jo, Sobrino Justin, Mitchell Grace S, Rentea Rebecca M
Comprehensive Colorectal Center, Department of Surgery, Children's Mercy Kansas City, Kansas City, MO 64108, USA.
Department of Radiology, Children's Mercy Kansas City, Kansas City, MO 64108, USA.
Case Rep Surg. 2021 Jan 12;2021:8870631. doi: 10.1155/2021/8870631. eCollection 2021.
Anorectal malformations (ARM) are complex disorders that often require staged reconstructions. We present a case and imaging findings of a child who developed issues following colostomy closure due to segmental colonic ischemia. . A 3-year-old female with Currarino syndrome presented with abdominal distention, blood-flecked stools, and prolonged cecostomy flush time. For her anorectal malformation, a colostomy was initially placed. A new colostomy was created at posterior sagittal anorectoplasty (PSARP) to allow the distal rectum to reach the anus without tension. Differentials for her presenting symptoms included a mislocation of the anus, stenosis at the anoplasty site, stricture within the colon, or sacral mass from Currarino syndrome, causing obstructive symptoms. Workup at our hospital included an anorectal exam under anesthesia (EUA), which showed a well-located anus with without stenosis at the anoplasty site, and an antegrade contrast study revealed a featureless descending colon with a 3-4 mm stricture in the distal transverse colon at the site of the previous colostomy, without an obstructing presacral mass. To alleviate this obstruction, the child underwent removal of the chronically ischemic descending colon and a redo-PSARP, where the distal transverse colon was brought down to the anus. She is now able to successfully perform antegrade flushes.
Patients who have had prior surgeries for ARM repair are at a higher risk of complications, including strictures or ischemic complications at areas of previous surgery or colostomy placement. A thorough preoperative workup, including contrast studies, can alert the surgeon to these potential pitfalls.
肛门直肠畸形(ARM)是复杂的疾病,通常需要分期重建。我们报告一例因节段性结肠缺血导致结肠造口关闭后出现问题的儿童病例及影像学表现。一名患有库拉里诺综合征的3岁女性出现腹胀、便血和盲肠造口冲洗时间延长。她最初因肛门直肠畸形接受了结肠造口术。在后方矢状位肛门直肠成形术(PSARP)时创建了一个新的结肠造口,以使远端直肠能够无张力地到达肛门。她出现这些症状的鉴别诊断包括肛门位置异常、肛门成形术部位狭窄、结肠内狭窄或库拉里诺综合征导致的骶骨肿块,从而引起梗阻症状。我院的检查包括麻醉下肛门直肠检查(EUA),结果显示肛门位置正常,肛门成形术部位无狭窄,顺行性造影研究显示降结肠无特征性改变,在先前结肠造口部位的远端横结肠有一处3 - 4毫米的狭窄,且无骶前占位性梗阻。为缓解这种梗阻,该患儿接受了慢性缺血降结肠切除术及再次PSARP手术,术中将远端横结肠下拉至肛门处。她现在能够成功进行顺行性冲洗。
既往接受过ARM修复手术的患者出现并发症的风险更高,包括先前手术或结肠造口部位的狭窄或缺血性并发症。全面的术前检查,包括造影研究,可以提醒外科医生注意这些潜在的陷阱。