Deviere J, Brohee D, Hiden M, Bourgeois N
Department of Gastroenterology, Hôpital Erasme, Brussel's Free University.
J Clin Gastroenterol. 1988 Feb;10(1):111-4. doi: 10.1097/00004836-198802000-00026.
In a woman with hereditary hemorrhagic telangiectasia (HHT) (Osler-Weber-Rendu disease) who died of fulminant hepatitis B, autopsy revealed cirrhosis of the liver and diffuse hepatic telangiectasia. Her daughter and grandson also suffered from the hepatic involvement of HHT. Sufficient laboratory investigations were available to exclude known causes of cirrhosis. We review the relationship between Osler-Weber-Rendu disease and liver cirrhosis or fibrosis.
一名患有遗传性出血性毛细血管扩张症（HHT，即奥斯勒-韦伯-伦杜病）的女性死于暴发性乙型肝炎，尸检发现肝脏硬化和弥漫性肝毛细血管扩张。她的女儿和孙子也患有HHT的肝脏病变。有足够的实验室检查排除已知的肝硬化病因。我们回顾了奥斯勒-韦伯-伦杜病与肝硬化或肝纤维化之间的关系。
