Zhang W, Dong L L, Zhu J, Liu Y Y, Zhao Y, Zeng X F, Zhang S Y
Department of Rheumatology, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences,National Clinical Research Center for Dermatologic and Immunologic Diseases, Beijing 100730, China.
Department of Rheumatology, Tongji Hospital,Tongji Medical College, Huazhong University of Science and Technology, Wuhan 430030, China.
Zhonghua Nei Ke Za Zhi. 2021 Mar 1;60(3):192-206. doi: 10.3760/cma.j.cn112138-20200803-00726.
IgG related disease (IgG-RD) is an immune medicated rare disease, characterized with chronic inflammation and fibrosis in the involved organs, it is a systemic disease affected nearly every anatomic site of the body, usually involvement of multiple organs, and with diverse clinical manifestations. Due to the the relative novelty of the disease and under-recognition, the overall level of diagnosis and treatment in China is uneven. Till now, there is no relevant expert consensus or guidance of IgG-RD in China. In order to further improve the understanding and standardize the management of IgG-RD, on the basis of summarizing domestic and international experience, the China Alliance For Rare Diseases, together with the Chinese Rheumatology Association, organized an expert group and established the Chinese expert consensus on the diagnosis and treatment of IgG related diseases.
IgG相关疾病(IgG-RD)是一种免疫介导的罕见病,其特征为受累器官出现慢性炎症和纤维化,是一种几乎累及身体每个解剖部位的全身性疾病,通常累及多个器官,且临床表现多样。由于该疾病相对新颖且认识不足,中国的整体诊疗水平参差不齐。目前,中国尚无IgG-RD的相关专家共识或指南。为进一步提高对IgG-RD的认识并规范其管理,中国罕见病联盟联合中华医学会风湿病学分会,在总结国内外经验的基础上,组织专家小组制定了IgG相关疾病诊断与治疗的中国专家共识。