Nojiri Gaku, Kamimori Tomoki, Uchiyama Mizuki, Tomyo Rei, Suga Yasushi, Takamori Kenji, Higo Ryuzaburo, Hayashi Ayato
Department of Plastic and Reconstructive Surgery, Juntendo University Urayasu Hospital, Chiba, Japan.
Department of Dermatology, Juntendo University Urayasu Hospital, Chiba, Japan.
Plast Reconstr Surg Glob Open. 2021 Feb 16;9(2):e3393. doi: 10.1097/GOX.0000000000003393. eCollection 2021 Feb.
Adenoid cystic carcinoma (ACC) is a relatively rare malignant tumor. It is more common in women than in men and typically develops in the lacrimal, salivary, and breast glands. ACC of the external auditory canal (EAC) is exceedingly rare, and its invasion into the ear lobe is even more unusual. In this report, we present a case of ACC that presented as a mass on the surface of the ear lobe in a 28-year-old woman and was initially diagnosed as infected atheroma. For wide resection of the tumor, half of the entire auricula was resected and superficial parotidectomy was performed. After confirming no tumor cells on the surface of the facial nerve, the defect was reconstructed by the combination of platysma muscle flap to prevent Frey syndrome and free forearm flap for the ear lobe form. There was no recurrence or metastasis of the tumor, and Frey syndrome did not occur at 2 years and 8 months after surgery. The patient was satisfied with the result, oncologically and cosmetically. Even in young patients, comprehensive treatments (including diagnosis, resection, and reconstruction) are important in painful ear lobe masses.
腺样囊性癌（ACC）是一种相对罕见的恶性肿瘤。女性比男性更常见，通常发生于泪腺、唾液腺和乳腺。外耳道腺样囊性癌极为罕见，侵犯耳垂更为异常。在本报告中，我们介绍了一例腺样囊性癌病例，该病例表现为一名28岁女性耳垂表面的肿块，最初被诊断为感染性粉瘤。为广泛切除肿瘤，切除了整个耳廓的一半并进行了腮腺浅叶切除术。在确认面神经表面无肿瘤细胞后，通过联合使用颈阔肌肌瓣预防味觉出汗综合征和游离前臂皮瓣修复耳垂外形来重建缺损。术后2年8个月，肿瘤无复发或转移，且未发生味觉出汗综合征。患者对肿瘤学和美容效果均满意。即使对于年轻患者，对于疼痛性耳垂肿块，综合治疗（包括诊断、切除和重建）也很重要。
