Department of Medicine, Uniformed Services University of the Health Sciences, Bethesda, MD, USA.
Department of Cardiology, Walter Reed National Military Medical Center, Bethesda, MD, USA.
J Osteopath Med. 2021 Mar 30;121(6):555-559. doi: 10.1515/jom-2020-0284.
This case report highlights the potentially underrecognized subtype of unilateral eosinophilic fasciitis (EF) in a 28 year old man. With fewer than 300 reported encounters to date, EF is a rare disease that eludes clinicians by presenting as a scleroderma like syndrome. As EF remains a clinical diagnosis, biopsy results may be nonspecific, and the disease can easily be misdiagnosed (or missed entirely) if a full thickness biopsy is not reviewed by a dermatopathologist. The authors also emphasize the importance of internationally accepted diagnostic criteria, of which at least two different sets exist.
本病例报告强调了一种在 28 岁男性中潜在的被低估的单侧嗜酸性筋膜炎(EF)亚型。EF 是一种罕见疾病,目前仅有不到 300 例报道,由于其表现为硬皮病样综合征,因此常被临床医生漏诊。由于 EF 仍然是一种临床诊断,活检结果可能不具有特异性,如果皮肤科病理学家没有对全层活检进行评估,那么该疾病很容易被误诊(或完全漏诊)。作者还强调了国际上公认的诊断标准的重要性,目前至少存在两套不同的标准。