Sakalihasan Sarah, Tchana-Sato Vincent, Courtois Audrey, Defraigne Jean Olivier, Sakalihasan Natzi
Department of Cardiovascular Surgery, CHU Liege, Liege, Belgium.
Acta Chir Belg. 2023 Feb;123(1):76-80. doi: 10.1080/00015458.2021.1910768. Epub 2021 Apr 8.
Isolated pulmonary artery vasculitis is an uncommon cause of pulmonary artery aneurysm with very few reported cases in the literature.
We hereby present the case of a 70-year-old man with occasional episodes of exertional chest discomfort. Our investigations revealed an expanding aneurysm of the main pulmonary artery extending to the proximal portion of the right branch. The patient successfully underwent replacement of the main pulmonary artery with a homograft.
Histopathological examination revealed images of vasculitis with numerous multinucleated giant cells. The patient's postoperative course was uneventful.
Management of pulmonary artery aneurysm secondary to isolated pulmonary artery vasculitis is not well studied, and no clear guidelines currently exist in the literature.
孤立性肺动脉血管炎是肺动脉瘤的一种罕见病因，文献报道的病例极少。
我们在此报告一名70岁男性患者，其偶发劳力性胸部不适。我们的检查发现主肺动脉有一个不断扩大的动脉瘤，延伸至右分支近端。该患者成功接受了同种异体移植主肺动脉置换术。
组织病理学检查显示血管炎图像，伴有大量多核巨细胞。患者术后过程顺利。
对于孤立性肺动脉血管炎继发的肺动脉瘤的治疗研究不足，目前文献中尚无明确的指导方针。
