Lenh Bui-Van, Duc Nguyen Minh, My Thieu-Thi Tra, Van Nguyen Dinh, Huong Bui-Thi My, Trung Hoang-Van, Bang Mai Tan Lien, Thong Pham Minh
Department of Radiology, Ha Noi Medical University, Ha Noi, Vietnam.
Department of Radiology, Pham Ngoc Thach University of Medicine, Ho Chi Minh City, Vietnam.
Radiol Case Rep. 2021 Apr 9;16(6):1352-1354. doi: 10.1016/j.radcr.2021.03.020. eCollection 2021 Jun.
Inflammatory myofibroblastic tumor (IMT) is an uncommon neoplasm that rarely arises in the genitourinary system. IMTs in the vulva in infants are extremely rare in the literature. The tumor consists of myofibroblastic spindle cells accompanied by inflammatory cell infiltration. In this article, we aimed to describe the case of IMT in the vulva. A newborn girl presented with a mass in the vulva detected in the prenatal period. The patient was treated with surgery and chemotherapy. Follow-up 8 months after surgery showed no signs of recurrence. In conclusion, IMT has a variable clinical presentation, surgery is the optimal approach, but in cases without complete resection, chemotherapy is essential.
炎性肌纤维母细胞瘤(IMT)是一种罕见的肿瘤,很少发生于泌尿生殖系统。婴儿外阴部的IMT在文献中极为罕见。该肿瘤由肌纤维母细胞性梭形细胞组成,并伴有炎症细胞浸润。在本文中,我们旨在描述外阴部IMT的病例。一名新生女婴在产前检查时发现外阴部有一肿块。该患者接受了手术及化疗治疗。术后8个月的随访显示无复发迹象。总之,IMT临床表现多样,手术是最佳治疗方法,但在未完全切除的病例中,化疗至关重要。