University of Florida, Gainesville, FL, USA.
J Investig Med High Impact Case Rep. 2021 Jan-Dec;9:23247096211014687. doi: 10.1177/23247096211014687.
Primary pulmonary artery sarcomas (PPAS) are extremely rare tumors that are often mislabeled as pulmonary emboli (PE). PPAS usually involve the pulmonary trunk and are histologically classified as leiomyosarcoma, spindle cells sarcoma, fibrous histiocytoma, or undifferentiated sarcoma. Our case involved a 78-year-old man with an undifferentiated PPAS confined to the left pulmonary artery that was initially misdiagnosed as a PE. After a month-long delay in treatment in which the patient was prescribed warfarin, the correct diagnosis was made. Pulmonary artery endarterectomy and left lung pneumonectomy were performed, and he survived for 18 months before disease recurrence and death. Our case helps illustrate some of the clinical and radiographic findings that help distinguish PPAS from PE.
原发性肺动脉肉瘤（PPAS）是一种极为罕见的肿瘤，常被误诊为肺栓塞（PE）。PPAS 通常累及肺动脉干，组织学上可分为平滑肌肉瘤、梭形细胞肉瘤、纤维组织细胞瘤或未分化肉瘤。本例为 78 岁男性，左肺动脉局限性未分化 PPAS，最初误诊为 PE。在给予华法林治疗一个月的延误后，才做出正确诊断。行肺动脉内膜切除术和左肺切除术，患者存活 18 个月后疾病复发并死亡。本病例有助于阐明一些有助于区分 PPAS 和 PE 的临床和影像学发现。
