Shin Christopher, Berliner Leonard
Department of Radiology, Northwell at Staten Island University Hospital, Staten Island, NY 11794, USA.
Radiol Case Rep. 2021 Apr 30;16(7):1643-1645. doi: 10.1016/j.radcr.2021.03.068. eCollection 2021 Jul.
Atypical or unilateral polycystic kidney disease is a rare entity that is found incidentally and is characterized on imaging as asymmetric or unilateral distribution of cysts confined to the kidneys. We present a case of an incidental finding of atypical polycystic kidney disease in a 72-year-old male. Computed tomography imaging showed asymmetric distribution of cysts only in the kidneys and the patient had no genitourinary symptoms, had normal renal function, and did not have a family history of renal disease. Although considered to be benign, rare cases of progression of atypical polycystic kidney disease to bilateral polycystic kidney disease has been documented in the literature, which portends a worse prognosis. It is important for clinicians to be aware of this entity so that patients can be monitored periodically for progression of disease.
非典型或单侧多囊肾病是一种罕见的疾病，通常偶然发现，其影像学特征为局限于肾脏的囊肿呈不对称或单侧分布。我们报告一例72岁男性偶然发现非典型多囊肾病的病例。计算机断层扫描成像显示囊肿仅在肾脏呈不对称分布，患者无泌尿生殖系统症状，肾功能正常，且无肾脏疾病家族史。尽管非典型多囊肾病被认为是良性的，但文献中已记录有罕见病例从非典型多囊肾病进展为双侧多囊肾病，这预示着预后更差。临床医生了解这种疾病很重要，以便能定期监测患者疾病的进展。
