Rabadão Tiago, Naia Leonor, Ferreira Filipa, Teixeira Mariana, Aveiro Marcelo, Eulálio Margarida, Silva Fernando
Internal Medicine Department Centro Hospitalar do Baixo Vouga Aveiro Portugal.
Hematology Department Centro Hospitalar do Baixo Vouga Aveiro Portugal.
Clin Case Rep. 2021 Mar 28;9(5):e04006. doi: 10.1002/ccr3.4006. eCollection 2021 May.
Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported.
噬血细胞性淋巴组织细胞增生症因缺乏特异性临床和实验室检查结果而造成诊断难题,在成人中尤为如此。尽管对该疾病的认识有所提高,但继发性特发性形式仍有报道。