Kern Medical Center, Bakersfield, CA, USA.
J Investig Med High Impact Case Rep. 2021 Jan-Dec;9:23247096211019558. doi: 10.1177/23247096211019558.
Acute pandysautonomia is a rare disorder characterized by autonomic failure affecting sympathetic, parasympathetic, and enteric functions. We present a case of acute inflammatory demyelinating polyneuropathy (AIDP) with severe pandysautonomia in a young, otherwise healthy, female who presented with gastrointestinal symptoms and sensory demyelinating polyneuropathy, which progressively worsened and subsequently developed bladder dysfunction and orthostatic hypotension. We discuss the challenges with diagnostic workup as well as the challenges we encountered as part of the management.
急性全自主神经功能衰竭是一种罕见的疾病，其特征为自主神经系统衰竭，影响交感神经、副交感神经和肠神经系统的功能。我们报告了一例年轻、健康的女性急性炎症性脱髓鞘性多发性神经病（AIDP）合并严重全自主神经功能衰竭的病例，该患者最初表现为胃肠道症状和感觉性脱髓鞘多发性神经病，病情逐渐恶化，随后出现膀胱功能障碍和直立性低血压。我们讨论了诊断评估中遇到的挑战以及作为管理的一部分我们所遇到的挑战。
