INSERM U1242, University of Rennes 1, Rennes, France.
Centre Eugène Marquis, Rennes, France.
Prog Mol Subcell Biol. 2021;59:197-214. doi: 10.1007/978-3-030-67696-4_10.
The endoplasmic reticulum, as the site of synthesis for proteins in the secretory pathway has evolved select machineries to ensure the correct folding and modification of proteins. However, sometimes these quality control mechanisms fail and proteins are misfolded. Other factors, such as nutrient deprivation, hypoxia or an increased demand on protein synthesis can also cause the accumulation of unfolded or misfolded proteins in the endoplasmic reticulum. There are mechanisms that recognise and deal with this accumulation of protein through degradation and/or export. Many diseases are associated with aberrant quality control mechanisms, and among these, cancer has emerged as a group of diseases that rely on endoplasmic reticulum homeostasis to sustain development and growth. The knowledge of how protein quality control operates in cancer has identified opportunities for these pathways to be pharmacologically targeted, which could lead to newer or more effective treatments in the future.
内质网是分泌途径中蛋白质合成的场所,它进化出了特定的机制来确保蛋白质的正确折叠和修饰。然而,有时这些质量控制机制会失效,导致蛋白质错误折叠。其他因素,如营养缺乏、缺氧或蛋白质合成需求增加,也会导致未折叠或错误折叠的蛋白质在内质网中积累。有一些机制可以识别和处理这种蛋白质的积累,通过降解和/或输出。许多疾病与异常的质量控制机制有关,其中癌症已成为一组依赖内质网稳态来维持其发育和生长的疾病。了解蛋白质质量控制在癌症中的作用,为这些途径的药物靶向提供了机会,这可能会导致未来出现更新或更有效的治疗方法。