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唇舌溃疡:一个不容忽视的不常见诊断。

Lipschütz Ulcer: An Unusual Diagnosis that Should Not be Neglected.

机构信息

Centro Hospitalar Barreiro-Montijo, Barreiro, Portugal.

出版信息

Rev Bras Ginecol Obstet. 2021 May;43(5):414-416. doi: 10.1055/s-0041-1729147. Epub 2021 Jun 2.

DOI:10.1055/s-0041-1729147
PMID:34077985
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10302062/
Abstract

The diagnosis of genital ulcers remains a challenge in clinical practice. Lipschütz ulcer is a non-sexually transmitted rare and, probably, underdiagnosed condition, characterized by the sudden onset of vulvar edema along with painful necrotic ulcerations. Despite its unknown incidence, this seems to be an uncommon entity, with sparse cases reported in the literature. We report the case of an 11-year-old girl who presented at the emergency department with vulvar ulcers. She denied any sexual intercourse. The investigation excluded sexually transmitted infections, so, knowledge of different etiologies of non-venereal ulcers became essential. The differential diagnoses are extensive and include inflammatory processes, drug reactions, trauma, and malignant tumors. Lipschütz ulcer is a diagnosis of exclusion. With the presentation of this case report, the authors aim to describe the etiology, clinical course, and outcomes of this rare disease, to allow differential diagnosis of genital ulceration.

摘要

生殖器溃疡的诊断在临床实践中仍然具有挑战性。Lipschütz 溃疡是一种非性传播的罕见疾病,可能存在诊断不足的情况,其特征为外阴突然出现水肿,并伴有疼痛性坏死性溃疡。尽管其发病率未知,但这种疾病似乎并不常见,文献中报道的病例很少。我们报告了一例 11 岁女孩的病例,她因外阴溃疡到急诊科就诊。她否认有任何性行为。检查排除了性传播感染,因此了解非性病性溃疡的不同病因至关重要。鉴别诊断范围广泛,包括炎症过程、药物反应、创伤和恶性肿瘤。Lipschütz 溃疡是一种排除性诊断。通过本病例报告的介绍,作者旨在描述这种罕见疾病的病因、临床过程和结局,以帮助鉴别诊断生殖器溃疡。

相似文献

1
Lipschütz Ulcer: An Unusual Diagnosis that Should Not be Neglected.唇舌溃疡:一个不容忽视的不常见诊断。
Rev Bras Ginecol Obstet. 2021 May;43(5):414-416. doi: 10.1055/s-0041-1729147. Epub 2021 Jun 2.
2
Lipschütz ulcer (ulcus vulvae acutum): a rare cause of genital lesion.利普许茨溃疡(急性女阴溃疡):生殖器病变的罕见病因。
An Bras Dermatol. 2012 Jul-Aug;87(4):622-4. doi: 10.1590/s0365-05962012000400018.
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Acute genital ulcers.急性生殖器溃疡
BMJ Case Rep. 2014 Jan 28;2014:bcr2013202504. doi: 10.1136/bcr-2013-202504.
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[Ulcer of Lipschütz, a diagnosis to consider in the pediatric population].[利普许茨溃疡,儿科人群中需考虑的一种诊断]
Arch Argent Pediatr. 2019 Jun 1;117(3):e305-e308. doi: 10.5546/aap.2019.e305.
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Lipschütz ulcer in a 17-month-old girl: a rare manifestation of Epstein-Barr primoinfection.17 个月大的女孩出现 Lipschütz 溃疡:EB 病毒原发感染的罕见表现。
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Lipschutz Ulcers in an Adolescent After Sars-CoV-2 Infection.青少年感染 SARS-CoV-2 后出现唇疱疹。
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[Lipschütz ulcus as a differential diagnosis of vulvar ulcus].[利普许茨溃疡作为外阴溃疡的鉴别诊断]
Ugeskr Laeger. 2018 Apr 2;180(14).
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[Acute vulvar ulcer of Lipschütz: a misdiagnosis entity].[利普许茨急性外阴溃疡:一种误诊疾病]
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Lipschütz Ulcers: A Rare Diagnosis in Women With Vulvar Ulceration.利普许茨溃疡:外阴溃疡女性中的罕见诊断。
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引用本文的文献

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Lipschütz Ulcers In 12-year-old Premenarchal Female Days After A Gastrointestinal Illness: A Case Report.一名12岁青春期前女性在患胃肠疾病数天后出现利普舒茨溃疡:病例报告
Clin Pract Cases Emerg Med. 2025 May;9(2):146-148. doi: 10.5811/cpcem.25343.
2
Adolescent female with vaginal pain.青春期女性,伴有阴道疼痛。
J Am Coll Emerg Physicians Open. 2024 May 3;5(3):e13181. doi: 10.1002/emp2.13181. eCollection 2024 Jun.
3
Lipschütz ulcers due to SARS-CoV-2 infection: a neglected diagnosis in emergency room.由新型冠状病毒2型(SARS-CoV-2)感染引起的利普舒茨溃疡:急诊室中被忽视的诊断。

本文引用的文献

1
Acute genital ulcers: keep Lipschütz ulcer in mind.急性生殖器溃疡:需考虑利普许茨溃疡。
Arch Gynecol Obstet. 2018 Nov;298(5):927-931. doi: 10.1007/s00404-018-4866-6. Epub 2018 Aug 24.
2
Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren's Syndrome.利普许茨生殖器溃疡作为原发性干燥综合征的首发表现
Case Rep Obstet Gynecol. 2018 Jun 3;2018:3507484. doi: 10.1155/2018/3507484. eCollection 2018.
3
Lipschütz Ulcers: A Rare Diagnosis in Women With Vulvar Ulceration.利普许茨溃疡:外阴溃疡女性中的罕见诊断。
Int J Womens Dermatol. 2024 Feb 12;10(1):e122. doi: 10.1097/JW9.0000000000000122. eCollection 2024 Mar.
4
Genital Ulcers Associated with Systemic Lupus Erythematosus - What are the Possible Causes? A Case Report.与系统性红斑狼疮相关的生殖器溃疡——可能的病因是什么?一例病例报告。
Eur J Case Rep Intern Med. 2023 Jul 29;10(8):003972. doi: 10.12890/2023_003972. eCollection 2023.
5
Lipschütz Ulcers: Classic Presentation of an Uncommon Condition.利普许茨溃疡:一种罕见病症的典型表现。
Cureus. 2023 May 3;15(5):e38505. doi: 10.7759/cureus.38505. eCollection 2023 May.
6
A Cohort Study to Compare Effects between Ulcer- and Nonulcer-Related Nonvariceal Upper Gastrointestinal Bleeding.一项比较溃疡相关性和非溃疡相关性非静脉曲张性上消化道出血之间效果的队列研究。
Appl Bionics Biomech. 2022 Jun 10;2022:3342919. doi: 10.1155/2022/3342919. eCollection 2022.
7
Recurrent reactive non-sexually related acute genital ulcers: a risk factor for Behcet's disease?复发性非性相关急性生殖器溃疡:贝赫切特病的一个危险因素?
Acta Biomed. 2022 Jun 6;93(S3):e2022196. doi: 10.23750/abm.v93iS3.13077.
Obstet Gynecol. 2017 Aug;130(2):420-422. doi: 10.1097/AOG.0000000000002145.
4
Lipschütz ulcers: uncommon diagnosis of vulvar ulcerations.利普许茨溃疡:外阴溃疡的罕见诊断。
BMJ Case Rep. 2016 Feb 15;2016:bcr2015214338. doi: 10.1136/bcr-2015-214338.
5
Lipschütz ulcers: should we rethink this? An analysis of 33 cases.利普许茨溃疡:我们是否应该重新审视它?33例病例分析。
Eur J Obstet Gynecol Reprod Biol. 2016 Mar;198:149-152. doi: 10.1016/j.ejogrb.2015.07.016. Epub 2015 Aug 6.
6
Genital ulcers: it is not always simplex ….生殖器溃疡:情况并不总是单纯的……
Int J STD AIDS. 2015 Jan;26(1):72-3. doi: 10.1177/0956462414541241. Epub 2014 Jun 26.
7
Ulcus vulvae acutum Lipschütz in two young female patients.利普许茨急性女阴溃疡,见于两名年轻女性患者。
Eur J Dermatol. 2014 May-Jun;24(3):361-4. doi: 10.1684/ejd.2014.2311.
8
Acute genital ulcers.急性生殖器溃疡
BMJ Case Rep. 2014 Jan 28;2014:bcr2013202504. doi: 10.1136/bcr-2013-202504.
9
Lipschütz ulcer (ulcus vulvae acutum): a rare cause of genital lesion.利普许茨溃疡(急性女阴溃疡):生殖器病变的罕见病因。
An Bras Dermatol. 2012 Jul-Aug;87(4):622-4. doi: 10.1590/s0365-05962012000400018.
10
Non-sexually related acute genital ulcers in 13 pubertal girls: a clinical and microbiological study.13名青春期女孩非性相关急性生殖器溃疡的临床与微生物学研究
Arch Dermatol. 2009 Jan;145(1):38-45. doi: 10.1001/archdermatol.2008.519.