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老年患者左心室心肌致密化不全心肌病的不寻常表现

An Unusual Presentation of Left Ventricular Non-compaction Cardiomyopathy in an Elderly Patient.

作者信息

Afify Hesham, Ghosh Somshukla, Khalil Melissa, Milunski Mark R

机构信息

Internal Medicine, University of Central Florida/HCA GME Consortium, Greater Orlando, USA.

Cardiology, Orlando Veterans Affairs Medical Center, Orlando, USA.

出版信息

Cureus. 2021 May 19;13(5):e15112. doi: 10.7759/cureus.15112.

DOI:10.7759/cureus.15112
PMID:34159015
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8212918/
Abstract

Left ventricular non-compaction cardiomyopathy (LVNC) is a rare cardiomyopathy. The true prevalence of LVNC is unclear. The clinical presentation of LVNC varies widely from asymptomatic to end-stage heart failure or sudden cardiac death, and the diagnostic criteria are not standardized. Moreover, there is an increased risk for thromboembolic events with LVNC. We present an unusual case of LVNC first diagnosed in a septuagenarian.

摘要

左心室致密化不全心肌病(LVNC)是一种罕见的心肌病。LVNC的真实患病率尚不清楚。LVNC的临床表现差异很大,从无症状到终末期心力衰竭或心源性猝死,且诊断标准不统一。此外,LVNC患者发生血栓栓塞事件的风险增加。我们报告了一例首次在一名七十多岁老人中诊断出的不寻常的LVNC病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3c35/8212918/1849a79dbb6f/cureus-0013-00000015112-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3c35/8212918/92a5de9493b3/cureus-0013-00000015112-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3c35/8212918/1849a79dbb6f/cureus-0013-00000015112-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3c35/8212918/92a5de9493b3/cureus-0013-00000015112-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3c35/8212918/1849a79dbb6f/cureus-0013-00000015112-i02.jpg

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本文引用的文献

1
Long-Term Survival of Patients With Left Ventricular Noncompaction.左心室心肌致密化不全患者的长期生存情况。
J Am Heart Assoc. 2021 Jan 19;10(2):e015563. doi: 10.1161/JAHA.119.015563. Epub 2021 Jan 14.
2
Left ventricular non-compaction as a potential source for cryptogenic ischemic stroke in the young: A case-control study.左心室致密化不全是年轻人隐源性缺血性卒中的潜在原因:一项病例对照研究。
PLoS One. 2020 Aug 14;15(8):e0237228. doi: 10.1371/journal.pone.0237228. eCollection 2020.
3
Prognostic Significance of Left Ventricular Noncompaction: Systematic Review and Meta-Analysis of Observational Studies.
左心室心肌致密化不全的预后意义:观察性研究的系统评价和荟萃分析。
Circ Cardiovasc Imaging. 2020 Jan;13(1):e009712. doi: 10.1161/CIRCIMAGING.119.009712. Epub 2020 Jan 21.
4
A systematic review and meta-analysis of the prevalence of left ventricular non-compaction in adults.成人左心室心肌致密化不全患病率的系统评价与荟萃分析。
Eur Heart J. 2020 Apr 7;41(14):1428-1436. doi: 10.1093/eurheartj/ehz317.
5
Meta-Analysis of the Prognostic Role of Late Gadolinium Enhancement and Global Systolic Impairment in Left Ventricular Noncompaction.左心室心肌致密化不全患者中晚期钆增强和整体收缩功能障碍的预后作用的荟萃分析。
JACC Cardiovasc Imaging. 2019 Nov;12(11 Pt 1):2141-2151. doi: 10.1016/j.jcmg.2018.12.029. Epub 2019 Mar 13.
6
Genotype-Positive Status Is Associated With Poor Prognoses in Patients With Left Ventricular Noncompaction Cardiomyopathy.基因型阳性与左心室心肌致密化不全患者预后不良相关。
J Am Heart Assoc. 2018 Oct 16;7(20):e009910. doi: 10.1161/JAHA.118.009910.
7
Anticoagulation Therapy in Specific Cardiomyopathies: Isolated Left Ventricular Noncompaction and Peripartum Cardiomyopathy.特定心肌病的抗凝治疗:孤立性左心室致密化不全和围生期心肌病。
J Cardiovasc Pharmacol Ther. 2019 Jan;24(1):31-36. doi: 10.1177/1074248418783745. Epub 2018 Jun 18.
8
Adult left ventricular noncompaction: reappraisal of current diagnostic imaging modalities.成人左心室心肌致密化不全:现行影像学诊断方式的再评估。
JACC Cardiovasc Imaging. 2014 Dec;7(12):1266-75. doi: 10.1016/j.jcmg.2014.09.005.
9
Reversible de novo left ventricular trabeculations in pregnant women: implications for the diagnosis of left ventricular noncompaction in low-risk populations.孕妇可逆性新出现的左室小梁:对低危人群左室致密化不全诊断的影响。
Circulation. 2014 Aug 5;130(6):475-83. doi: 10.1161/CIRCULATIONAHA.114.008554. Epub 2014 Jul 8.
10
An interesting case of cryptogenic stroke in a young man due to left ventricular non-compaction: role of cardiac MRI in the accurate diagnosis.一名年轻男性因左心室心肌致密化不全导致的不明原因卒中的有趣病例:心脏磁共振成像在准确诊断中的作用
BMJ Case Rep. 2014 Jun 24;2014:bcr2014204230. doi: 10.1136/bcr-2014-204230.