Doege-Potter 综合征：文献系统回顾及罕见盆腔恶性孤立性纤维瘤病例报告
Doege-Potter syndrome: a systematic review of the literature and case presentation of a rare pelvic malignant solitary fibrous tumour.
机构信息
School of Women and Children's Health, Faculty of Medicine, University of New South Wales, Sydney, New South Wales, Australia
Obstetrics and Gynaecology, The Royal Hospital for Women, Randwick, New South Wales, Australia.
出版信息
BMJ Case Rep. 2021 Aug 19;14(8):e242447. doi: 10.1136/bcr-2021-242447.
Abstract
Solitary fibrous tumours (SFTs) are a rare mesenchymal neoplasm with an incidence of 2.8 per 100 000 of which only 1% occur in the female genital tract. Doege-Potter syndrome is a paraneoplastic phenomenon associated with approximately 5%-10% of SFTs and is characterised by non-islet cell hypoglycaemia due to tumour production of low molecular weight insulin-like growth factor-II. We present the fourth confirmed case of female pelvic SFT with Doege-Potter syndrome and a literature review.
摘要
孤立性纤维瘤（SFT）是一种罕见的间叶性肿瘤，发病率为每 10 万人 2.8 例，其中只有 1%发生在女性生殖道。Doege-Potter 综合征是一种副瘤现象，约占 SFT 的 5%-10%，其特征是非胰岛细胞瘤低血糖症，由于肿瘤产生低分子量胰岛素样生长因子-II。我们报告了第四例女性盆腔 SFT 合并 Doege-Potter 综合征，并进行了文献复习。
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本文引用的文献
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