Almuqamam Mohamed, Ebrahim Mohamed, Nassar George, Kaplan Matthew
Pediatrics, The Brooklyn Hospital Center, New York, USA.
Pediatric Nephrology, The Brooklyn Hospital Center, New York, USA.
Cureus. 2021 Aug 16;13(8):e17221. doi: 10.7759/cureus.17221. eCollection 2021 Aug.
Retro-aortic left renal vein (RLRV) is an anatomical variation, where the left renal vein (LRV) courses posterior to the aorta and anterior to the vertebrae before it eventually drains into the inferior vena cava (IVC). RLRV is a rare finding, with a prevalence of around 1%-2%, and only a small minority of RLRVs cause symptoms. RLRV symptoms occur secondary to compression of the LRV between the abdominal aorta and vertebrae, otherwise known as posterior nutcracker syndrome (PNCS). The most common symptoms of PNCS are hematuria and flank pain. We present a 17-year-old male, who came in with recurring left flank pain without hematuria, initially thought to be renal colic secondary to nephrolithiasis. On further investigations, an aberrant posterior renal vein was seen on CT suggestive of PNCS. The patient was treated successfully with RLRV vascular stent placement by interventional radiology. This case report adds to the limited number of PNCS cases observed in children and to the even rarer cases of PNCS without hematuria. This case also acts as a reminder for pediatricians to keep a wide scope of differentials in patients presenting with flank pain and provides an outline of both diagnostic and treatment modalities available for these patients.
主动脉后左肾静脉(RLRV)是一种解剖变异,即左肾静脉(LRV)在汇入下腔静脉(IVC)之前,走行于主动脉后方和椎体前方。RLRV是一种罕见的情况,发生率约为1%-2%,只有一小部分RLRV会引起症状。RLRV症状继发于腹主动脉和椎体之间的左肾静脉受压,即所谓的胡桃夹综合征(PNCS)。PNCS最常见的症状是血尿和侧腹痛。我们报告一名17岁男性,因反复出现左侧侧腹痛但无血尿前来就诊,最初被认为是肾结石继发的肾绞痛。进一步检查发现,CT显示异常的后肾静脉,提示PNCS。该患者通过介入放射学成功进行了RLRV血管支架置入治疗。本病例报告增加了儿童PNCS病例的有限数量,以及更罕见的无血尿PNCS病例。该病例也提醒儿科医生,对于出现侧腹痛的患者要进行广泛的鉴别诊断,并提供了这些患者可用的诊断和治疗方法概述。