Institute of Biophysics and Biomedical Engineering, Bulgarian Academy of Sciences, Acad. G. Bonchev, 1113 Sofia, Bulgaria.
Department of Neurology, University Multiprofile Hospital for Active Treatment in Neurology and Psychiatry Sv. Naum, 1113 Sofia, Bulgaria.
Biomolecules. 2021 Oct 12;11(10):1500. doi: 10.3390/biom11101500.
The main trend of current research in neurodegenerative diseases (NDDs) is directed towards the discovery of novel biomarkers for disease diagnostics and progression. The pathological features of NDDs suggest that diagnostic markers can be found in peripheral fluids and cells. Herein, we investigated the thermodynamic behavior of the peripheral red blood cells (RBCs) derived from patients diagnosed with three common NDDs-Parkinson's disease (PD), Alzheimer's disease (AD), and amyotrophic lateral sclerosis (ALS) and compared it with that of healthy individuals, evaluating both fresh and aged RBCs. We established that NDDs can be differentiated from the normal healthy state on the basis of the variation in the thermodynamic parameters of the unfolding of major RBCs proteins-the cytoplasmic hemoglobin (Hb) and the membrane Band 3 (B3) protein. A common feature of NDDs is the higher thermal stability of both Hb and B3 proteins along the RBCs aging, while the calorimetric enthalpy can distinguish PD from ALS and AD. Our data provide insights into the RBCs thermodynamic behavior in two complex and tightly related phenomena-neurodegenerative pathologies and aging, and it suggests that the determined thermodynamic parameters are fingerprints of the altered conformation of Hb and B3 protein and modified RBCs' aging in the studied NDDs.
当前神经退行性疾病(NDDs)研究的主要趋势是发现用于疾病诊断和进展的新型生物标志物。NDDs 的病理特征表明,诊断标志物可以在外周液和细胞中找到。在此,我们研究了来自被诊断为三种常见 NDDs(帕金森病(PD)、阿尔茨海默病(AD)和肌萎缩侧索硬化症(ALS)的患者的外周红细胞(RBC)的热力学行为,并将其与健康个体进行了比较,同时评估了新鲜和老化的 RBC。我们确定,根据主要 RBC 蛋白(细胞质血红蛋白(Hb)和膜带 3(B3)蛋白的展开热力学参数的变化,可以将 NDD 与正常健康状态区分开来。NDD 的一个共同特征是 Hb 和 B3 蛋白在 RBC 老化过程中的热稳定性更高,而量热焓可以区分 PD、ALS 和 AD。我们的数据深入了解了 RBC 在两种复杂且紧密相关的现象中的热力学行为——神经退行性病变和衰老,并表明所确定的热力学参数是 Hb 和 B3 蛋白构象改变以及所研究 NDDs 中 RBC 老化的特征指纹。