Tsujimura Ryusuke, Sato Daisuke, Obikane Hiyo, Kawachi Riken, Sugitani Masahiko, Hao Hiroyuki, Sakurai Hiroyuki, Yamakawa Mitsunori, Masuda Shinobu
Department of Pathology, Nihon University School of Medicine Tokyo, Japan.
Department of Respiratory Surgery, Nihon University School of Medicine Tokyo, Japan.
Int J Clin Exp Pathol. 2021 Oct 15;14(10):1061-1064. eCollection 2021.
Rosai-Dorfman disease is a rare disorder of histiocytic proliferation in lymph nodes and at extranodal sites. We herein describe a patient with isolated Rosai-Dorfman disease in the thymus with elevated anti-acetylcholine receptor antibody. We examined the relationship between Rosai-Dorfman disease and elevated anti-acetylcholine receptor antibody. To our knowledge, elevated anti-acetylcholine receptor antibody has not been reported in isolated thymic Rosai-Dorfman disease.
罗萨伊-多夫曼病是一种罕见的组织细胞在淋巴结及结外部位增殖的疾病。我们在此描述一例胸腺孤立性罗萨伊-多夫曼病患者,其抗乙酰胆碱受体抗体升高。我们研究了罗萨伊-多夫曼病与抗乙酰胆碱受体抗体升高之间的关系。据我们所知,孤立性胸腺罗萨伊-多夫曼病中抗乙酰胆碱受体抗体升高尚未见报道。