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病例报告:“一名年轻成年人昏迷的意外病因”

Case report: "an unexpected origin of coma in a young adult".

作者信息

Chandrikasing Ranjana, Ramnarain Sudeshkoemar, Bansie Rakesh, Yang Harvey, Ponssen Huibert, Ramdhani Navin

机构信息

Intensive Care at Academic Hospital Paramaribo, Paramaribo, Suriname.

Resident Emergency Medicine at Academic Hospital Paramaribo, Paramaribo, Suriname.

出版信息

Int J Emerg Med. 2021 Nov 27;14(1):70. doi: 10.1186/s12245-021-00390-5.

DOI:10.1186/s12245-021-00390-5
PMID:34837945
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8903714/
Abstract

We report a peculiar case of acute non-traumatic coma due to neuromuscular hypoventilation syndrome caused by a non-traumatic spinal cord injury (NTSCI). A 21-year-old patient presented to the emergency room complaining of sudden onset weakness in his lower limbs and shortness of breath. While in the ER, he briefly became comatose and labs revealed an acute respiratory acidosis. Detailed neurologic examination ultimately revealed upper motor neuron signs and quadriplegia. He was ultimately diagnosed with a non-traumatic spinal cord injury, in particular, a cervical transverse myelitis which had caused acute diaphragmatic weakness. Although a very rare cause of coma, emergency medicine physicians need to be aware of transverse myelitis, a disorder that may result in rapidly progressive neurologic decline and is treated with immunomodulation.

摘要

我们报告了一例因非创伤性脊髓损伤(NTSCI)导致神经肌肉通气不足综合征引起的急性非创伤性昏迷的特殊病例。一名21岁患者因下肢突然无力和呼吸急促前往急诊室就诊。在急诊室时,他短暂昏迷,实验室检查显示急性呼吸性酸中毒。详细的神经系统检查最终发现上运动神经元体征和四肢瘫痪。他最终被诊断为非创伤性脊髓损伤,特别是颈段横贯性脊髓炎,该疾病导致了急性膈肌无力。尽管横贯性脊髓炎是导致昏迷的非常罕见的原因,但急诊医学医生需要了解这种疾病,它可能导致迅速进展的神经功能衰退,需通过免疫调节进行治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb9b/8903714/71a1a4c5c596/12245_2021_390_Fig2_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb9b/8903714/956319fe9240/12245_2021_390_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb9b/8903714/71a1a4c5c596/12245_2021_390_Fig2_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb9b/8903714/956319fe9240/12245_2021_390_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb9b/8903714/71a1a4c5c596/12245_2021_390_Fig2_HTML.jpg

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本文引用的文献

1
Longitudinally extensive transverse myelitis with pulmonary tuberculosis: Two case reports.伴有肺结核的纵向广泛横贯性脊髓炎:两例报告
Medicine (Baltimore). 2018 Jan;97(3):e9676. doi: 10.1097/MD.0000000000009676.
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Successfully Managed Acute Transverse Myelitis Related to Scrub Typhus and Serial Image Findings.成功治疗与恙虫病相关的急性横贯性脊髓炎及系列影像表现
Am J Trop Med Hyg. 2017 Mar;96(3):557-560. doi: 10.4269/ajtmh.16-0524. Epub 2017 Apr 6.
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A young woman with numbness in her feet.一位双脚麻木的年轻女子。
JAAPA. 2016 Dec;29(12):38-40. doi: 10.1097/01.JAA.0000508204.02557.9a.
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Longitudinally extensive transverse myelitis as presenting manifestation of small cell carcinoma lung.纵向广泛横贯性脊髓炎作为小细胞肺癌的首发表现
Oxf Med Case Reports. 2015 Feb 26;2015(2):208-10. doi: 10.1093/omcr/omv011. eCollection 2015 Feb.
5
Longitudinally extensive transverse myelitis with intramedullary metastasis of small-cell lung carcinoma: an autopsy case report.小细胞肺癌髓内转移所致纵向广泛横贯性脊髓炎:一例尸检病例报告
Case Rep Neurol Med. 2013;2013:305670. doi: 10.1155/2013/305670. Epub 2013 Dec 22.
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Transverse myelitis--a review of the presentation, diagnosis, and initial management.横贯性脊髓炎——临床表现、诊断及初始治疗综述
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7
Case report of transverse myelitis in a patient receiving etanercept for rheumatoid arthritis.一名接受依那西普治疗类风湿关节炎的患者发生横贯性脊髓炎的病例报告。
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Pupillary evaluation for differential diagnosis of coma.用于昏迷鉴别诊断的瞳孔评估。
Postgrad Med J. 2003 Jan;79(927):49-51. doi: 10.1136/pmj.79.927.49.