Acharya Suman, Kandel Suraj, Shrestha Suraj, Tiwari Sansar Babu, Sapkota Subash, Bhattarai Anjan, Jha Saket
Department of Internal Medicine Tribhuvan University Teaching Hospital Kathmandu Nepal.
Institute of Medicine Maharajgunj Medical Campus Kathmandu Nepal.
Clin Case Rep. 2021 Nov 22;9(11):e05132. doi: 10.1002/ccr3.5132. eCollection 2021 Nov.
Barraquer-Simons syndrome is a rare entity characterized by progressive loss of subcutaneous tissue in the face and/or upper half of the body and can be associated with autoimmune conditions such as systemic lupus erythematosus. Close long-term follow-up is required to identify metabolic disturbances, potentially life-threatening renal problems, and other associated diseases.
巴拉奎尔-西蒙斯综合征是一种罕见病症,其特征为面部和/或身体上半部分的皮下组织进行性丧失,且可能与自身免疫性疾病如系统性红斑狼疮相关。需要进行密切的长期随访,以识别代谢紊乱、潜在危及生命的肾脏问题及其他相关疾病。