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并发应激性心肌病的重症肌无力危象

A Myasthenic Crisis Complicated by a Takotsubo Cardiomyopathy.

作者信息

Ramrattan Amit, Gonzalez Iovank, Abdullah Harun, Maraj Kevin, Browne Mariana

机构信息

Internal Medicine, Port of Spain General Hospital, Port of Spain, TTO.

Internal Medicine/Cardiology, Port of Spain General Hospital, Port of Spain, TTO.

出版信息

Cureus. 2022 Jan 10;14(1):e21067. doi: 10.7759/cureus.21067. eCollection 2022 Jan.

DOI:10.7759/cureus.21067
PMID:35036232
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8752402/
Abstract

Myasthenia gravis (MG) is an autoimmune disorder of the neuromuscular junction that affects skeletal muscles causing weakness, typically the ocular, facial, oropharyngeal, respiratory, and limb muscles. Patients can present as either an MG exacerbation with weakness of any muscle group or an MG crisis which is a life-threatening weakness of the respiratory muscles that usually requires intubation and mechanical ventilation; however, though rare, cardiac manifestations must be considered in the management of such patients.

摘要

重症肌无力(MG)是一种神经肌肉接头处的自身免疫性疾病,会影响骨骼肌,导致肌肉无力,通常累及眼部、面部、口咽、呼吸及肢体肌肉。患者可能表现为任何肌肉群无力导致的重症肌无力加重,或者重症肌无力危象,即呼吸肌无力,这是一种危及生命的情况,通常需要插管和机械通气;然而,尽管罕见,但在这类患者的管理中必须考虑心脏表现。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/f140b008a0ee/cureus-0014-00000021067-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/7e1f5fa2efac/cureus-0014-00000021067-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/5991e35f52a4/cureus-0014-00000021067-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/0c2e46f2c4fc/cureus-0014-00000021067-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/f140b008a0ee/cureus-0014-00000021067-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/7e1f5fa2efac/cureus-0014-00000021067-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/5991e35f52a4/cureus-0014-00000021067-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/0c2e46f2c4fc/cureus-0014-00000021067-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e4b7/8752402/f140b008a0ee/cureus-0014-00000021067-i04.jpg

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引用本文的文献

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Myasthenic crisis-induced Takotsubo cardiomyopathy: a case report.重症肌无力危象诱发的应激性心肌病:一例报告
Ann Med Surg (Lond). 2024 Jan 15;86(3):1704-1707. doi: 10.1097/MS9.0000000000001723. eCollection 2024 Mar.
2
Takotsubo Cardiomyopathy and Autoimmune Disorders: A Systematic Scoping Review of Published Cases.心肌心尖球形综合征与自身免疫性疾病:已发表病例的系统范围回顾。
Int J Clin Pract. 2024 Feb 20;2024:7259200. doi: 10.1155/2024/7259200. eCollection 2024.
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A Case Report and 31-Case Study: Does Takotsubo Cardiomyopathy in Myasthenia Gravis Patients Have a High Mortality Rate?

本文引用的文献

1
Takotsubo syndrome in patients with myasthenia gravis: a systematic review of previously reported cases.Takotsubo 综合征在重症肌无力患者中的表现:对既往报道病例的系统回顾。
BMC Neurol. 2019 Nov 12;19(1):281. doi: 10.1186/s12883-019-1523-z.
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International Expert Consensus Document on Takotsubo Syndrome (Part I): Clinical Characteristics, Diagnostic Criteria, and Pathophysiology.国际 Takotsubo 综合征专家共识文件(第一部分):临床特征、诊断标准和病理生理学。
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一例病例报告及31例病例研究:重症肌无力患者的应激性心肌病死亡率高吗?
Cureus. 2022 Aug 31;14(8):e28625. doi: 10.7759/cureus.28625. eCollection 2022 Aug.
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Current state of knowledge on Takotsubo syndrome: a Position Statement from the Taskforce on Takotsubo Syndrome of the Heart Failure Association of the European Society of Cardiology.Takotsubo 综合征的现有知识状况:欧洲心脏病学会心力衰竭协会 Takotsubo 综合征工作组的立场声明。
Eur J Heart Fail. 2016 Jan;18(1):8-27. doi: 10.1002/ejhf.424. Epub 2015 Nov 9.
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World J Cardiol. 2014 Jul 26;6(7):602-9. doi: 10.4330/wjc.v6.i7.602.
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Clinical characteristics and cardiovascular magnetic resonance findings in stress (takotsubo) cardiomyopathy.应激(心碎)性心肌病的临床特征和心血管磁共振成像表现。
JAMA. 2011 Jul 20;306(3):277-86. doi: 10.1001/jama.2011.992.
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Stress (Takotsubo) cardiomyopathy--a novel pathophysiological hypothesis to explain catecholamine-induced acute myocardial stunning.应激(应激性心肌病)——一种解释儿茶酚胺诱导的急性心肌顿抑的新病理生理假说。
Nat Clin Pract Cardiovasc Med. 2008 Jan;5(1):22-9. doi: 10.1038/ncpcardio1066.
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Takotsubo cardiomyopathy or transient left ventricular apical ballooning syndrome: A systematic review.应激性心肌病或短暂性左心室心尖气球样变综合征:一项系统综述。
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