Department of Thoracic Surgery, Okayama University Hospital.
Acta Med Okayama. 2022 Feb;76(1):89-92. doi: 10.18926/AMO/63217.
Congenital lobar emphysema (CLE) is defined as the hyperinflation of pulmonary lobes due to obstruction of the flow of air via a known or unknown etiology, which causes pressure symptoms in the adjacent organs. CLE is mainly diagnosed in the neonatal period, and very few adult cases have been reported. Here we report a 34-year-old male with muscular dystrophy who was diagnosed with CLE on examination. He underwent a right lower lobectomy via 3-portal completely video-assisted thoracoscopic surgery, and his symptoms improved. Thoracoscopic surgery helped preserve the respiratory muscles and led to the improvement of respiratory function in this patient.
先天性肺大疱（CLE）是指由于已知或未知病因导致空气流动受阻，使肺叶过度充气而引起的疾病，可导致邻近器官受压。CLE 主要发生在新生儿期，仅有少数成人病例报道。本文报告了 1 例 34 岁男性，患有肌肉萎缩症，体格检查诊断为 CLE。患者接受了 3 孔完全电视辅助胸腔镜下右下肺叶切除术，术后症状改善。胸腔镜手术有助于保留呼吸肌，改善了患者的呼吸功能。
