Department of Pulmonary, King Khalid National Guard Hospital, King Abdul Aziz Medical City, Jeddah, Saudi Arabia.
Ann Thorac Med. 2008 Apr;3(2):60-3. doi: 10.4103/1817-1737.39639.
Hypogenetic lung syndrome is more popularly known as a scimitar syndrome (SS). It is a rare developmental lung malformation which almost always occurs on the right side. The two most constant features of this syndrome are anomalous pulmonary venous return into systemic circulation, most frequently via inferior vena cava (IVC), and lung hypoplasia.We are reporting such a case illustrating most typical and some uncommon features on chest radiograph and multislice computer tomography (MSCT) of chest. Focal herniation of liver through a diaphragmatic defect presenting as an ovoid soft tissue mass in right lower paraspinal region on chest X ray mimicking sequestration is an interesting but rare finding.
肺发育不全综合征又称弯刀综合征（SS）。它是一种罕见的肺发育畸形，几乎总是发生在右侧。该综合征的两个最常见特征是异常肺静脉回流至体循环，最常见的途径是下腔静脉（IVC），以及肺发育不全。我们报告了这样一个病例，该病例在胸部 X 线和胸部多层计算机断层扫描（MSCT）上显示了最典型和一些不常见的特征。通过膈肌缺陷出现的肝脏局限性疝出，在右侧下后脊柱旁区域呈现为卵圆形软组织肿块，类似于隔离肺，这是一种有趣但罕见的发现。
