Jabbouri Rajaa, Bouanani Nouama, Aniq Filali Rita, Aasfara Jehanne
Department of Internal Medicine, Mohammed VI University of Health Sciences (UM6SS), Casablanca, MAR.
Department of Haematology, Mohammed VI University of Health Sciences (UM6SS), Casablanca, MAR.
Cureus. 2022 Apr 6;14(4):e23896. doi: 10.7759/cureus.23896. eCollection 2022 Apr.
Eosinophilic fasciitis (EF) or Shulman's fasciitis is a rare condition characterized by subcutaneous edematous induration sparing the face and distal extremities and progressing to skin sclerosis. Its association with other pathologies, notably hemopathies, is described in the literature, but its association with smoldering multiple myeloma remains very rare, especially in a younger subject.
嗜酸性筋膜炎(EF)或舒尔曼筋膜炎是一种罕见病症,其特征为面部和四肢远端无皮下水肿性硬结,并进展为皮肤硬化。文献中描述了它与其他病理状况,尤其是血液系统疾病的关联,但它与冒烟型多发性骨髓瘤的关联仍然非常罕见,特别是在较年轻的患者中。