Shanghai Institute of Hematology, State Key Laboratory of Medical Genomics, National Research Center for Translational Medicine at Shanghai, Ruijin Hospital Affiliated to Shanghai Jiao Tong University School of Medicine, Shanghai.
Shanghai Institute of Hematology, State Key Laboratory of Medical Genomics, National Research Center for Translational Medicine at Shanghai, Ruijin Hospital Affiliated to Shanghai Jiao Tong University School of Medicine, Shanghai, China; CNRS-LIA Hematology and Cancer, Sino-French Research Center for Life Sciences and Genomics, Ruijin Hospital Affiliated to Shanghai Jiao Tong University School of Medicine, Shanghai.
Haematologica. 2022 Nov 1;107(11):2589-2600. doi: 10.3324/haematol.2021.280147.
Patients with newly diagnosed acute promyelocytic leukemia (APL) are often obese or overweight, accompanied by metabolic disorders, such as dyslipidemia. However, the link between dyslipidemia and leukemia is obscure. Here, we conducted a retrospective study containing 1,412 cases (319 newly diagnosed APL patients, 393 newly diagnosed non-APL acute myeloid leukemia patients, and 700 non-tumor controls) and found that APL patients had higher triglyceride levels than non- APL and control groups. Using clinical data, we revealed that hypertriglyceridemia served as a risk factor for early death in APL patients, and there was a positive correlation between triglyceride levels and leukocyte counts. RNA sequencing analysis of APL patients having high or normal triglyceride levels highlighted the contribution of peroxisome proliferatoractivated receptor-α (PPARα), a crucial regulator of cell metabolism and a transcription factor involved in cancer development. The genome-wide chromatin occupancy of PPARα revealed that PPARα co-existed with PML/RARα within the super-enhancer regions to promote cell proliferation. PPARα knockdown affected the expression of target genes responsible for APL proliferation, including FLT3, and functionally inhibited the proliferation of APL cells. Moreover, in vivo results in mice having high fat diet-induced high triglyceride levels supported the connection between high triglyceride levels and the leukemic burden, as well as the involvement of PPARα-mediated-FLT3 activation in the proliferation of APL cells. Our findings shed light on the association between APL proliferation and high triglyceride levels and provide a genetic link to PPARα-mediated hyperlipidemia in APL.
新诊断的急性早幼粒细胞白血病 (APL) 患者常伴有肥胖或超重,同时伴有代谢紊乱,如血脂异常。然而,血脂异常与白血病之间的联系尚不清楚。在这里,我们进行了一项回顾性研究,包含 1412 例病例(319 例新诊断的 APL 患者,393 例新诊断的非 APL 急性髓系白血病患者,700 例非肿瘤对照),发现 APL 患者的甘油三酯水平高于非 APL 和对照组。使用临床数据,我们揭示了高甘油三酯血症是 APL 患者早期死亡的危险因素,甘油三酯水平与白细胞计数呈正相关。对甘油三酯水平高或正常的 APL 患者进行 RNA 测序分析,突出了过氧化物酶体增殖物激活受体-α (PPARα) 的作用,PPARα 是细胞代谢的关键调节剂,也是癌症发展涉及的转录因子。PPARα 的全基因组染色质占有率表明,PPARα 与 PML/RARα 一起存在于超增强子区域,促进细胞增殖。PPARα 的敲低影响了负责 APL 增殖的靶基因的表达,包括 FLT3,并在功能上抑制了 APL 细胞的增殖。此外,在高脂肪饮食诱导甘油三酯水平升高的小鼠体内实验结果支持了高甘油三酯水平与白血病负担之间的联系,以及 PPARα 介导的 FLT3 激活在 APL 细胞增殖中的作用。我们的研究结果揭示了 APL 增殖与高甘油三酯水平之间的关联,并为 APL 中 PPARα 介导的高脂血症提供了遗传联系。