Magalhães Ana, Moreira Inês, Pinheiro Sofia, Borba Alexandra
Pulmonology Department. Hospital de Santa Marta. Centro Hospitalar Universitário Lisboa Central. Lisboa. Portugal.
Internal Medicine Department. Hospital Santo António dos Capuchos. Centro Hospitalar Universitário Lisboa Central. Lisboa. Portugal.
Acta Med Port. 2023 Feb 1;36(2):122-126. doi: 10.20344/amp.16896. Epub 2022 May 13.
We present a case of a 33-year-old male who worked as a plumber and a locksmith. The patient presented with diffuse myalgia and asthenia, skin sclerosis and puffy fingers, Raynaud's phenomenon, exertional dyspnea and erectile dysfunction. The presence of specific autoantibodies enabled the diagnosis of systemic sclerosis. Chest-computed tomography revealed upper lobe consolidation. After extensive evaluation, the multidisciplinary interstitial lung disease team concluded that the patient also had advanced silicosis. After a year, there was significant clinical, radiologic, and functional deterioration of the lung disease. The patient was referred for lung transplant. Silica inhalation is the cause of silicosis but is also implicated in the development of systemic sclerosis (Erasmus syndrome). Although they share a common risk factor, it is rare to find both diseases co-existing. We present this case of a young patient where both diseases presented aggressively in order to raise awareness to this association.
我们报告一例33岁男性病例,该患者从事水管工和锁匠工作。患者表现为弥漫性肌痛和乏力、皮肤硬化和手指肿胀、雷诺现象、劳力性呼吸困难和勃起功能障碍。特异性自身抗体的存在有助于诊断系统性硬化症。胸部计算机断层扫描显示上叶实变。经过广泛评估,多学科间质性肺病团队得出结论,该患者还患有晚期矽肺。一年后,肺部疾病出现了显著的临床、放射学和功能恶化。该患者被转诊进行肺移植。吸入二氧化硅是矽肺的病因,但也与系统性硬化症(伊拉斯谟综合征)的发生有关。尽管它们有共同的危险因素,但两种疾病同时存在的情况很少见。我们报告这例年轻患者两种疾病均呈侵袭性表现的病例,以提高对这种关联的认识。