Contini Giorgia, Frediani Simone, Pardi Valerio, Diomedi-Camassei Francesca, Inserra Alessandro
General and Thoracic Pediatric Surgery Unit, Bambino Gesù Children's Hospital, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS), Rome, Italy.
Pathology Unit, Department of Laboratories, Bambino Gesù Children's Hospital, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS), Rome, Italy.
Front Pediatr. 2022 May 18;10:898038. doi: 10.3389/fped.2022.898038. eCollection 2022.
Cystic dysplasia of the rete testis (CDRT) is a rare cause of testicular masses in children. The pathogenesis of this malformation remains unclear. It is often associated with other genitourinary anomalies, commonly presenting as agenesis or dysplasia of the ipsilateral kidney. A case involving a 9-year-old boy with a testicular lesion and ipsilateral renal agenesis, who was diagnosed with CDRT after histological examination, is reported. In addition, a systematic review of the literature was performed to better understand this pathology to design the most appropriate treatment and follow-up strategy for patients with CDRT.
睾丸网囊性发育异常(CDRT)是儿童睾丸肿块的罕见病因。这种畸形的发病机制尚不清楚。它常与其他泌尿生殖系统异常相关,通常表现为同侧肾脏发育不全或发育异常。本文报告了一例9岁男孩,患有睾丸病变及同侧肾缺如,经组织学检查诊断为CDRT。此外,还对文献进行了系统回顾,以更好地了解这种病理情况,从而为CDRT患者设计最合适的治疗和随访策略。