Wojcik L J, Hansen K, Diamond D A, Koyle M, Koff S A, Coplen D E, Caldamone A A
Hasbro Children's Hospital, Rhode Island Hospital, Providence, USA.
J Urol. 1997 Aug;158(2):600-4. doi: 10.1016/s0022-5347(01)64566-x.
Cystic dysplasia of the rete testis is a benign congenital lesion that can mimic testicular cancer. We report 6 cases, review the literature, discuss the embryological etiology and make management recommendations.
The records and pathology reports of 6 boys presenting with cystic dysplasia of the rete testis at 5 institutions were reviewed, as was the relevant literature.
Of the 6 cases 5 presented as scrotal masses in previously healthy boys and 1 as an abdominal mass in a newborn with multiple congenital anomalies. One patient had been followed from birth for a multicystic dysplastic kidney and 4 were found to have an ipsilateral absent kidney during evaluation. Development of the contralateral side was normal in most cases.
Cystic dysplasia of the rete testis is an unusual, benign congenital lesion that can mimic testicular cancer in presentation. The presence of ipsilateral renal anomalies, particularly renal agenesis, can suggest cystic dysplasia of the rete testis in the differential diagnosis preoperatively. Even if cystic dysplasia of the rete testis is suspected, we recommend inguinal exploration and early control of the spermatic cord in the event that neoplasia is identified. If possible, the goal of preserving as much normal testicular parenchyma as possible is desirable. Long-term followup for possible recurrence is recommended, particularly after local excision.
睾丸网囊性发育异常是一种可酷似睾丸癌的良性先天性病变。我们报告6例病例，复习相关文献，讨论胚胎学病因并提出处理建议。
回顾了5家机构中6例表现为睾丸网囊性发育异常的男孩的病历及病理报告，并复习了相关文献。
6例中，5例表现为阴囊肿物，患儿此前身体健康，1例表现为腹部肿物，为1名患有多种先天性异常的新生儿。1例患者自出生起因多囊性发育不良肾接受随访，4例在评估过程中发现同侧肾缺如。多数情况下对侧肾脏发育正常。
睾丸网囊性发育异常是一种不常见的良性先天性病变，其表现可酷似睾丸癌。同侧肾异常，尤其是肾缺如，在术前鉴别诊断中可提示睾丸网囊性发育异常。即便怀疑为睾丸网囊性发育异常，我们建议行腹股沟探查术，一旦发现肿瘤则尽早控制精索。若有可能，目标是尽可能保留更多正常睾丸实质。建议进行长期随访以观察有无可能复发，尤其是在局部切除术后。
