硬皮病与间质性肺疾病——病例报告
Scleroderma and interstitial lung disease - A case report.
作者信息
Gul Fahad, Siddiqui Amna, Srikaram Prakhyath, Fatima Nabeela
机构信息
Rawalpindi Medical University, Rawalpindi, Pakistan.
Karachi Medical and Dental College, Karachi City, Sindh, 74700, Pakistan.
出版信息
Ann Med Surg (Lond). 2022 Jul 9;80:104143. doi: 10.1016/j.amsu.2022.104143. eCollection 2022 Aug.
BACKGROUND
Systemic sclerosis with interstitial lung disease is one of the rarely reported autoimmune disorders. The ILD associated with systemic sclerosis is the most common cause of mortality in these patients.
CASE PRESENTATION
A 37-year-old female patient who is a known case of Scleroderma, Cor pulmonale, and hypothyroidism presented with the exacerbated symptoms of dyspnea and orthopnea. On examination, she had digital gangrene as a dermatological complication of systemic sclerosis. The patient was given medical management and was improving.
DISCUSSION
ILD is the dreaded complication of systemic sclerosis. Pulmonary hypertension that developed secondary to the ILD in this patient led to the cor pulmonale. The patient has the exacerbation of the same.
CONCLUSION
Early detection and management of the ILD-SS are very important to prevent progression, exacerbations, and morbidity associated with it.
背景
系统性硬化症合并间质性肺病是一种鲜有报道的自身免疫性疾病。与系统性硬化症相关的间质性肺病是这些患者最常见的死亡原因。
病例介绍
一名37岁女性患者，已知患有硬皮病、肺心病和甲状腺功能减退症，出现呼吸困难和气促症状加重。检查发现，她有手指坏疽，这是系统性硬化症的一种皮肤并发症。该患者接受了药物治疗，病情正在好转。
讨论
间质性肺病是系统性硬化症可怕的并发症。该患者因间质性肺病继发的肺动脉高压导致了肺心病。患者病情加重。
结论
早期发现和治疗系统性硬化症合并间质性肺病对于预防其进展、加重及相关发病率非常重要。
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