Abalı Hülya, Tokgöz Akyıl Fatma, Tural Önür Seda, Akanıl Fener Neslihan, Ölçmen Aysun
Clinic of Chest Diseases, Yedikule Chest Diseases and Thoracic Surgery Training and Research Hospital, İstanbul, Turkey.
Department of Pathology, Yedikule Chest Diseases and Thoracic Surgery Training and Research Hospital, İstanbul, Turkey.
Turk Thorac J. 2022 Jul;23(4):302-305. doi: 10.5152/TurkThoracJ.2022.21273.
Pulmonary sclerosing pneumocytoma is a rare, low-grade pulmonary tumor observed as unilateral or bilateral multiple nodules at a rate of 4%-5%. Among the autoimmune connective tissue disorders, those most commonly associated with lung malignancies are sclero- derma and rheumatoid arthritis. In this study, we report a rare case of a 55-year-old middle-aged Asian woman with slow-growing bilat- eral multiple pulmonary sclerosing pneumocytoma and scleroderma-rheumatoid arthritis overlap syndrome. The autoimmune disorders and pulmonary fibrosis of this case might have led to the development of PSP.
肺硬化性细胞瘤是一种罕见的低度肺肿瘤，以4%-5%的比例表现为单侧或双侧多发结节。在自身免疫性结缔组织疾病中，最常与肺恶性肿瘤相关的是硬皮病和类风湿关节炎。在本研究中，我们报告了一例罕见病例，一名55岁的亚洲中年女性，患有生长缓慢的双侧多发肺硬化性细胞瘤以及硬皮病-类风湿关节炎重叠综合征。该病例的自身免疫性疾病和肺纤维化可能导致了肺硬化性细胞瘤的发生。
