Ugonabo Onyinye, Mohamed Mujtaba, Frandah Wesam, Sherif Ahmed
Division of Gastroenterology, Department of Medicine, Joan C. Edwards School of Medicine, Marshall University, Huntington, WV 25701, USA.
J Med Cases. 2022 Jul;13(7):313-317. doi: 10.14740/jmc3930. Epub 2022 Jun 16.
Dysphagia lusoria (DL) is a rare clinical entity caused by compression of the esophagus by an aberrant right subclavian artery. It is coined from the Latin word meaning freak or jest of nature, with an estimated prevalence of approximately 0.5%. Before the term DL was known, the artery abnormality was referred to as luxus nature. Most patients are asymptomatic. In 30-40% of cases, DL results in tracheoesophageal symptoms like dysphagia to solid foods, chest pain, cough, and Horner's syndrome. Symptoms presenting later in life have been linked to arteriosclerosis and diminishing esophageal compliance resulting in compression. Another reason why people become symptomatic is due to Kommerell's diverticulum, a disorder that was first described by Kommerell, a German radiologist in 1936. It is also known as lusoria diverticulum, remnant diverticulum or lusoria root. This disorder represents a remnant of the left dorsal arch which forms a vascular ring behind the esophagus, leading to external compression. The key to diagnosis of DL is a barium esophagogram which may show extrinsic compression. Computed tomography or magnetic resonance imaging can be used for definite delineation of the vascular anatomy. Treatment approach is dietary modification or surgical intervention for unresponsive cases. Here, we present cases of dysphagia in two middle-aged women caused by compression effect on the esophagus by an aberrant right subclavian artery who did not respond to dietary modification.
迷走右锁骨下动脉压迫所致吞咽困难(DL)是一种罕见的临床病症。该名称源自拉丁语,意为大自然的怪异或玩笑,估计患病率约为0.5%。在DL这一术语出现之前,这种动脉异常被称为先天性血管变异。大多数患者无症状。在30% - 40%的病例中,DL会导致气管食管症状,如固体食物吞咽困难、胸痛、咳嗽和霍纳综合征。晚年出现的症状与动脉硬化和食管顺应性降低导致压迫有关。人们出现症状的另一个原因是科默雷尔憩室,这是一种由德国放射科医生科默雷尔于1936年首次描述的病症。它也被称为先天性憩室、残余憩室或先天性根部。这种病症代表左背主动脉弓的残余部分,在食管后方形成血管环,导致外部压迫。DL诊断的关键是钡餐食管造影,其可能显示外部压迫。计算机断层扫描或磁共振成像可用于明确血管解剖结构。治疗方法是调整饮食,对于无反应的病例则进行手术干预。在此,我们介绍两例中年女性因迷走右锁骨下动脉对食管的压迫作用导致吞咽困难且对饮食调整无反应的病例。