Ansari Ghassem, Mansouri Mahsa, Eftekhar Leila
Department of Pediatric Dentistry, Dental School, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Department of Pediatric Dentistry, Dental School, Alborz University of Medical Sciences, Karaj, Iran.
Front Dent. 2021 Jun 29;18:21. doi: 10.18502/fid.v18i21.6931. eCollection 2021.
Pulmonary atresia with ventricular septal defect (PA/VSD) is one of the congenital heart diseases that results in cyanosis, susceptibility to bacterial endocarditis, and increased risk of complications during general anesthesia. Glucose-6-phosphate dehydrogenase (G6PD) deficiency is the most common inherited genetic disorder affecting the red blood cells. We aimed to elaborate the potential dental management for patients with this serious condition. This report presents the single-visit dental treatment of a three-year-old female with PA/VSD, G6PD deficiency and rampant caries. The complexity of dental treatments, high incidence of dental caries, lack of cooperation, and the systemic condition limit treatment options to providing service under general anesthesia and hospitalization. Careful monitoring of oxygen saturation during general anesthesia and antibiotic prophylaxis are essential due to the invasive nature of dental treatments. It appears that single-visit dental management under general anesthesia minimizes the risk of treatment of patients at high risk of bacterial endocarditis.
肺动脉闭锁合并室间隔缺损（PA/VSD）是导致发绀、易患细菌性心内膜炎以及全身麻醉期间并发症风险增加的先天性心脏病之一。葡萄糖-6-磷酸脱氢酶（G6PD）缺乏症是影响红细胞的最常见遗传性疾病。我们旨在阐述针对患有这种严重疾病患者的潜在牙科治疗方法。本报告介绍了一名患有PA/VSD、G6PD缺乏症和猖獗龋齿的三岁女性的单次就诊牙科治疗情况。牙科治疗的复杂性、龋齿的高发病率、缺乏合作以及全身状况限制了治疗选择，只能在全身麻醉和住院情况下提供服务。由于牙科治疗具有侵入性，因此在全身麻醉期间仔细监测血氧饱和度以及预防性使用抗生素至关重要。全身麻醉下的单次就诊牙科治疗似乎将细菌性心内膜炎高风险患者的治疗风险降至最低。
