Hernández-Pérez Daniela, Butrón-Téllez Girón Claudia, Ruiz-Rodríguez Socorro, Garrocho-Rangel Arturo, Pozos-Guillén Amaury
Pediatric Dentistry Postgraduate Program, Faculty of Dentistry, San Luis Potosi University, 2 Dr. Manuel Nava, Zona Universitaria, 78290 San Luis Potosí, SLP, Mexico.
Case Rep Dent. 2015;2015:506459. doi: 10.1155/2015/506459. Epub 2015 Sep 7.
Glucose-6-phosphate dehydrogenase (G6PD) deficiency is an uncommon inherited enzyme deficiency characterized by hemolytic anemia, caused by the inability of erythrocytes to detoxify oxidizing agents such as drugs, infectious diseases, or fava bean ingestion. In this later case, the disorder is known as favism. The aim of the present report was to present a review of the literature in this disease, to describe a case report concerning an affected 9-year-old male, and to review the main implications and precautions in pediatric dental management.
葡萄糖-6-磷酸脱氢酶(G6PD)缺乏症是一种罕见的遗传性酶缺乏症,其特征为溶血性贫血,这是由于红细胞无法对药物、传染病或食用蚕豆等氧化剂进行解毒所致。在后一种情况下,该病症被称为蚕豆病。本报告的目的是对该疾病的文献进行综述,描述一例9岁患病男性的病例报告,并探讨儿科牙科管理中的主要影响因素和注意事项。