Ellis G S, Frey T, Gouterman R Z
J Pediatr Ophthalmol Strabismus. 1987 May-Jun;24(3):111-9. doi: 10.3928/0191-3913-19870501-04.
Six patients with the syndrome of myelinated nerve fibers, high axial myopia, and refractory amblyopia were studied with particular emphasis on their sensory status. Ocular examination included keratometry, B-scan ultrasonography, measurement of axial lengths, and fundus photography. Sensory testing included visual fields, photostress testing, and neutral density filter visual acuities. Electrophysiological testing was also performed on some patients. Our findings suggest an organic etiology for the poor vision, although all patients had superimposed functional amblyopia as well. We suggest that myelination about the macula is the most likely cause of this poor vision and that the myelination, in some way, may have stimulated the development of the high myopia.
对6例患有有髓神经纤维综合征、高度轴性近视和难治性弱视的患者进行了研究，特别关注他们的感觉状态。眼部检查包括角膜曲率测量、B超超声检查、眼轴长度测量和眼底照相。感觉测试包括视野检查、光应激测试和中性密度滤光片视力测试。还对部分患者进行了电生理测试。我们的研究结果表明，尽管所有患者都同时存在功能性弱视，但视力不佳存在器质性病因。我们认为黄斑周围的髓鞘形成是导致视力不佳的最可能原因，并且这种髓鞘形成可能在某种程度上刺激了高度近视的发展。
