门静脉血栓形成作为阵发性睡眠性血红蛋白尿的首发表现。
Portal vein thrombosis as the first presentation of paroxysmal nocturnal hemoglobinuria.
机构信息
Department of Gastroenterology, General Hospital of Northern Theater Command, Shenyang, China.
Department of Hepatobiliary Surgery, General Hospital of Northern Theater Command, Shenyang, China.
出版信息
Drug Discov Ther. 2022 Sep 17;16(4):200-203. doi: 10.5582/ddt.2022.01033. Epub 2022 Aug 21.
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, acquired clonal hematopoietic stem cell disorder, characterized by hemolytic anemia, bone marrow failure and thrombosis. Portal vein thrombosis (PVT) is relatively rare in patients with PNH. In this paper, we reported PVT as the first clinical presentation of PNH in a female patient. PVT related symptoms resolved after anticoagulation therapy.
阵发性睡眠性血红蛋白尿症（PNH）是一种罕见的获得性克隆性造血干细胞疾病，其特征为溶血性贫血、骨髓衰竭和血栓形成。门静脉血栓形成（PVT）在 PNH 患者中相对罕见。本文报道了 1 例以 PVT 为 PNH 首发表现的女性患者，经抗凝治疗后 PVT 相关症状缓解。
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