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小儿非神经管闭合性髓内脂肪瘤:两例报告及文献复习

Pediatric Nondysraphic Intramedullary Lipoma : Report of Two Cases and Review of the Literature.

作者信息

Lee Jong Seok, Kim Young Mi, Chae Soo Ahn, Kim Seung-Ki, Phi Ji Hoon

机构信息

Division of Pediatric Neurosurgery, Seoul National University Children's Hospital, Seoul National University College of Medicine, Seoul, Korea.

Department of Pediatrics, Pusan National University Hospital, Pusan National University School of Medicine and Biochemical Research Institute, Busan, Korea.

出版信息

J Korean Neurosurg Soc. 2023 Mar;66(2):211-218. doi: 10.3340/jkns.2022.0156. Epub 2022 Sep 8.

DOI:10.3340/jkns.2022.0156
PMID:36071566
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10009248/
Abstract

Pediatric nondysraphic intramedullary lipoma is very rare, and only limited cases have been reported. In the present case, we present two infant patients with these pathologies who were surgically treated. Previous literature on 20 patients with these diseases who had undergone surgical treatments was analyzed. Surgical treatment should be considered in most symptomatic patients, and laminoplastic laminotomy and internal debulking of the lipoma under intraoperative neurophysiological monitoring are mostly recommended.

摘要

小儿非脊髓纵裂性髓内脂肪瘤非常罕见,仅有有限的病例报道。在本病例中,我们介绍了两名患有这些病症并接受手术治疗的婴儿患者。分析了之前20例接受手术治疗的此类疾病患者的文献。大多数有症状的患者应考虑手术治疗,术中神经生理监测下的椎板成形椎板切开术和脂肪瘤内减压术是最常推荐的方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d61/10009248/62e288f0a18f/jkns-2022-0156f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d61/10009248/58d637ebbd9e/jkns-2022-0156f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d61/10009248/62e288f0a18f/jkns-2022-0156f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d61/10009248/58d637ebbd9e/jkns-2022-0156f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d61/10009248/62e288f0a18f/jkns-2022-0156f2.jpg

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本文引用的文献

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Turk Arch Pediatr. 2021 Jan 1;56(1):85-87. doi: 10.14744/TurkPediatriArs.2020.90187. eCollection 2021 Jan.
2
Maximal Resection of Intramedullary Lipoma Using Intraoperative Ultrasonography: A Technical Note.使用术中超声对髓内脂肪瘤进行最大程度切除:技术要点
Acta Med Okayama. 2021 Apr;75(2):239-242. doi: 10.18926/AMO/61907.
3
A Rare Case of Intramedullary Lipoma of Brainstem to Thoracic Cord--What to Do?一例罕见的脑干至胸段脊髓髓内脂肪瘤——该如何处理?
J Pediatr Neurosci. 2020 Apr-Jun;15(2):145-149. doi: 10.4103/jpn.JPN_134_19. Epub 2020 Jun 27.
4
Thoracic Intramedullary Lipoma in a 3-year-old Child: Spontaneous Decrease in the Size Following Incomplete Resection.一名3岁儿童的胸椎髓内脂肪瘤:不完全切除后肿瘤大小自发缩小
Asian J Neurosurg. 2018 Jan-Mar;13(1):188-190. doi: 10.4103/1793-5482.180965.
5
Neurosurgical management and pathology of lumbosacral lipomas with tethered cord.伴脊髓栓系的腰骶部脂肪瘤的神经外科治疗与病理学
Neuropathology. 2017 Oct;37(5):385-392. doi: 10.1111/neup.12382. Epub 2017 Apr 7.
6
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