D'Amico Raíssa Campos, Ziliotto Tamara Marques, Ávila Rayssa Marquesa, Paes Stela Kremmer Bezerra, Sampaio José, Guarinello Giovanna Golin, da Silva Jéssica Prado
Santa Casa de Curitiba, Departamento de Cirurgia Vascular, Curitiba, PR, Brasil.
J Vasc Bras. 2022 Sep 19;21:e20210129. doi: 10.1590/1677-5449.202101291. eCollection 2022.
Inferior vena cava leiomyosarcomas are rare tumors that account for less than 0.7% of all retroperitoneal leiomyosarcomas. They are more common in women and cause nonspecific chronic abdominal pain. In this report, we present the case of a 53-year-old female patient complaining of chronic nonspecific periumbilical abdominal pain with initial onset 8 months previously who was diagnosed with inferior vena cava leiomyosarcoma by computed tomography angiography. The patient was treated with complete resection of the tumor and reconstruction of the inferior vena cava with interposition of a Dacron prosthetic graft. The treatment considered the gold standard consists of complete surgical excision, because these tumors are resistant to chemotherapy and radiotherapy. The prognosis of these patients is closely related to early diagnosis. Therefore, it is very important that vascular and general surgeons know that this disease is a possible differential diagnosis of chronic abdominal pains.
下腔静脉平滑肌肉瘤是罕见肿瘤,占所有腹膜后平滑肌肉瘤的比例不到0.7%。它们在女性中更为常见,可引起非特异性慢性腹痛。在本报告中,我们介绍了一例53岁女性患者,她主诉脐周慢性非特异性腹痛,最初发病于8个月前,通过计算机断层血管造影被诊断为下腔静脉平滑肌肉瘤。该患者接受了肿瘤完全切除,并使用涤纶人工血管置换进行下腔静脉重建。被认为是金标准的治疗方法是完全手术切除,因为这些肿瘤对化疗和放疗耐药。这些患者的预后与早期诊断密切相关。因此,血管外科医生和普通外科医生了解这种疾病是慢性腹痛的一种可能鉴别诊断非常重要。