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下腔静脉平滑肌肉瘤:术前诊断与手术治疗

Inferior vena cava leiomyosarcoma: preoperative diagnosis and surgical management.

作者信息

Moncayo Karla Elizabeth, Vidal-Insua Juan José, Troncoso Ana, García Raúl

机构信息

Complejo Hospitalario Universitario de Pontevedra, Mourente s/n, Pontevedra, 36071, Spain.

出版信息

Surg Case Rep. 2015 Dec;1(1):35. doi: 10.1186/s40792-015-0036-2. Epub 2015 Apr 10.

Abstract

Inferior vena cava (IVC) leiomyosarcoma is a rare malignant neoplasm more commonly seen in women in the fifth to sixth decade of life. Complete resection of the tumor with negative margins is the only therapeutical option that has demonstrated a survival benefit. This report presents a case of a 67-year-old woman affected by a lower segment IVC leiomyosarcoma incidentally detected during a chronic abdominal pain study. The patient was treated with tumorectomy, resection and ligation of the infrarenal IVC without signs or recurrence on a 12-month follow-up.

摘要

下腔静脉平滑肌肉瘤是一种罕见的恶性肿瘤,多见于50至60岁的女性。肿瘤切缘阴性的完整切除是唯一已证明有生存获益的治疗选择。本报告介绍了一例67岁女性病例,该患者在慢性腹痛检查中偶然发现患有下段下腔静脉平滑肌肉瘤。患者接受了肿瘤切除术、肾下腔静脉切除及结扎术,12个月的随访中无复发迹象。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5f64/4747934/96b29edc2ec1/40792_2015_36_Fig1_HTML.jpg

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