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特发性结肠气囊样积气症:气腹的一种罕见病因。

Idiopathic pneumatosis cystoides coli: An uncommon cause of pneumoperitoneum.

作者信息

Peixoto André, Pereira Rafaela, Leitão João

机构信息

Serviço de Imagiologia Geral, Centro Hospitalar Universitário Lisboa Norte, Avenida Professor Egas Moniz, Lisboa 1649-035, Portugal.

出版信息

Radiol Case Rep. 2022 Sep 19;17(11):4408-4412. doi: 10.1016/j.radcr.2022.08.067. eCollection 2022 Nov.

DOI:10.1016/j.radcr.2022.08.067
PMID:36188071
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9520510/
Abstract

Pneumatosis cystoides intestinalis (PCI) is a rare entity characterized by the presence of gaseous cystic within the intestinal wall. The primary or idiopathic type represents 15% of cases and is a self-limited or chronic benign entity. The secondary type represents 85% of cases and is associated with various factors, such as surgery, pharmacotherapy, chemotherapy, autoimmune diseases, inflammatory diseases, and pulmonary illness. Pneumatosis cystoides intestinalis affects the colon (pneumatosis cystoides coli) in about half of the cases. The differential diagnosis of PCI includes potentially life-threatening diseases that cause pneumatosis intestinalis. The misdiagnosis of PCI is common and can lead to unnecessary treatments and surgical procedures. We describe an asymptomatic pneumoperitoneum incidentally seen on chest radiograph. The cause was pneumatosis cystoides coli, which did not require treatment.

摘要

肠气囊肿症(PCI)是一种罕见疾病,其特征为肠壁内存在气体性囊肿。原发性或特发性类型占病例的15%,是一种自限性或慢性良性疾病。继发性类型占病例的85%,与多种因素相关,如手术、药物治疗、化疗、自身免疫性疾病、炎症性疾病和肺部疾病。肠气囊肿症约半数病例累及结肠(结肠气囊肿症)。PCI的鉴别诊断包括可导致肠积气的潜在危及生命的疾病。PCI的误诊很常见,可能导致不必要的治疗和手术操作。我们描述了一例胸部X线片偶然发现的无症状气腹。病因是结肠气囊肿症,无需治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/8f83f2cb5fcf/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/86371a5730a5/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/2bc32acf78de/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/d1f32c0842ab/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/8f83f2cb5fcf/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/86371a5730a5/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/2bc32acf78de/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/d1f32c0842ab/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0d90/9520510/8f83f2cb5fcf/gr4.jpg

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Pneumatosis cystoides intestinalis: a case report and literature review.肠气肿症:一例病例报告并文献复习。
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Benign versus life-threatening causes of pneumatosis intestinalis: differentiating CT features.肠壁积气的良性与危及生命病因:CT特征鉴别
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Pneumatosis cystoides intestinalis: six case reports and a review of the literature.肠壁囊样积气症:6例报告及文献复习
BMC Gastroenterol. 2018 Jun 28;18(1):100. doi: 10.1186/s12876-018-0794-y.
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