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温德利希综合征的不典型表现。

Unusual Presentation of Wünderlich Syndrome.

作者信息

García-Chairez Luis R, Montelongo-Rodríguez Fred A, Moreno-Arquieta Ilse A, Ayala Max Molina, Gutierrez-González Adrián

机构信息

Department of Urology, Hospital Universitario Dr. José Eleuterio González, Universidad Autónoma de Nuevo León, Monterrey, Nuevo León, México.

Medical School Universidad Autónoma de Nuevo León, Monterrey, Nuevo León, México.

出版信息

Ochsner J. 2022 Fall;22(3):273-276. doi: 10.31486/toj.21.0120.

Abstract

Wünderlich syndrome is a rare but important condition because it involves a sudden blood collection in the renal fossa that can cause hemodynamic instability. A 38-year-old female with a history of type 2 diabetes mellitus and hypertension with poor adherence to treatment presented to the emergency department with abdominal pain of 2 weeks' duration accompanied by irritative lower urinary symptoms. Abdominal computed tomography (CT) scan showed bilateral pyelonephritis and an abscess in the lower pole of the right kidney. A second CT scan, performed because of the patient's abrupt decrease in hemoglobin and hematocrit, showed active bleeding secondary to the infectious process in the right kidney. The patient was hemodynamically unstable, so a nephrectomy was performed. Wünderlich syndrome is a spontaneous renal hemorrhage, in most cases attributed to a tumorous etiology and rarely of infectious origin. The clinical picture is varied but can present with the Lenk triad of acute onset flank pain, flank mass, and hypovolemic shock. It is diagnosed principally via an imaging study such as abdominal CT scan. Treatment is conservative in principle, but urgent surgical intervention is sometimes necessary depending on the clinical situation of the patient.

摘要

温德利希综合征是一种罕见但重要的病症,因为它涉及肾窝内突然出血,可导致血流动力学不稳定。一名38岁女性,有2型糖尿病和高血压病史,治疗依从性差,因持续2周的腹痛伴刺激性下尿路症状就诊于急诊科。腹部计算机断层扫描(CT)显示双侧肾盂肾炎和右肾下极脓肿。由于患者血红蛋白和血细胞比容突然下降而进行的第二次CT扫描显示,右肾感染过程继发活动性出血。患者血流动力学不稳定,因此进行了肾切除术。温德利希综合征是一种自发性肾出血,在大多数情况下归因于肿瘤病因,很少由感染引起。临床表现多样,但可出现急性发作的胁腹痛、胁腹肿块和低血容量性休克的Lenk三联征。主要通过腹部CT扫描等影像学检查进行诊断。原则上治疗是保守的,但根据患者的临床情况,有时需要紧急手术干预。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c38b/9477127/40d6f361f04c/toj-21-0120-figure1.jpg

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