Acharya Sourya, Andhale Amol, Shukla Samarth, Bhansali Pratik J, Kabra Ruchita, Kumar Sunil
Department of Medicine, Jawaharlal Nehru Medical College, Datta Meghe Institute of Medical Sciences (Deemed to be University), Wardha, IND.
Department of Medicine, Jawaharlal Nehru Medical College, Wardha, IND.
Cureus. 2022 Sep 6;14(9):e28838. doi: 10.7759/cureus.28838. eCollection 2022 Sep.
Dyke-Davidoff-Masson syndrome (DDMS) is a rare condition that usually presents in early life with recurrent seizures. It can be congenital or can be acquired by perinatal hypoxia, infections, and intracranial hemorrhage. Its frequency remains unknown. It is usually diagnosed by neuroimaging. The classical neuroimaging features are unilateral cerebral hemiatrophy, volume loss, and hyperpneumatization of the sinus. We present the case of a 22-year-old male who presented with complex partial status epilepticus and had a history of recurrent seizures since he was six years old. The diagnosis of DDMS was made on neuroimaging.
戴克-戴维多夫-马森综合征(DDMS)是一种罕见疾病,通常在早年出现反复癫痫发作。它可以是先天性的,也可由围产期缺氧、感染和颅内出血所致。其发病率尚不清楚。通常通过神经影像学检查来诊断。典型的神经影像学特征是单侧大脑半球萎缩、体积减小和鼻窦过度气化。我们报告一例22岁男性病例,该患者表现为复杂部分性癫痫持续状态,自6岁起就有反复癫痫发作史。通过神经影像学检查确诊为DDMS。