Al-Smair Ali, Abdel Hafez Sufian, Saadeh Ahmad, Al-Ali Ahmad
Department of Radiology, Medray International Radiology Center, Amman, JOR.
Faculty of Medicine, The University of Jordan, Amman, JOR.
Cureus. 2022 Mar 19;14(3):e23315. doi: 10.7759/cureus.23315. eCollection 2022 Mar.
Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease affecting the brain with almost 100 cases previously reported, with only 21 cases among adults. Due to the intricacy of clinical manifestations and radiological findings, it is difficult to reach the diagnosis. It usually includes atrophy of the cerebral hemisphere, dilation of the lateral ventricle, hypertrophy of skull bones, and hyperpneumatization of air sinuses. Herein, we present a case of a 55-year-old female patient who presented with a new-onset seizure. This case emphasizes the importance of considering DDMS in the differential diagnosis of adult-onset seizures, especially in patients with a previous history of brain insult, and demonstrates the possibility of developing this condition despite the lack of childhood symptoms. To our knowledge, this is the first case reported in Jordan.
戴克-戴维多夫-马森综合征(DDMS)是一种罕见的脑部疾病,此前报道的病例近100例,其中成人病例仅21例。由于临床表现和影像学检查结果复杂,难以确诊。它通常包括脑半球萎缩、侧脑室扩张、颅骨肥大和气窦过度气化。在此,我们报告一例55岁女性患者,该患者新发癫痫发作。该病例强调了在成人癫痫发作的鉴别诊断中考虑DDMS的重要性,特别是对于有脑损伤既往史的患者,并证明了即使没有儿童期症状也可能发生这种疾病。据我们所知,这是约旦报道的首例病例。