遗传性主动脉病变患者主动脉弓的外科治疗
Surgical management of the aortic arch in patients with inherited aortopathy.
作者信息
Lucchese Gianluca, Bilkhu Rajdeep
机构信息
Department of Cardiac Surgery, St Thomas' Hospital, London, United Kingdom.
出版信息
Front Cardiovasc Med. 2022 Oct 20;9:974190. doi: 10.3389/fcvm.2022.974190. eCollection 2022.
Surgical management of the aortic root and ascending aorta has seen an evolution over the past 50 years. Despite the widely available guidelines for management of the aortic root and ascending aorta, including in those with connective tissue disease and inherited aortopathies, there are generally no clear guideline indications for when to intervene on the aortic arch in these patients. This perhaps may be related to the fact that whilst the majority of acquired aortopathies, and also in non-syndromic aortopathies such as in bicuspid aortic valve, size criteria are utilized to decide on when to intervene, the use of size criteria may not be appropriate in those with syndromic inherited aortopathies. The aim of the present mini review is to provide a general overview and guidance for the surgical management of patients with inherited aortopathies.
在过去50年里，主动脉根部和升主动脉的外科治疗发生了演变。尽管有广泛可用的主动脉根部和升主动脉管理指南，包括针对患有结缔组织病和遗传性主动脉病变的患者，但对于这些患者何时干预主动脉弓，通常没有明确的指南指征。这可能与以下事实有关：虽然大多数后天性主动脉病变，以及诸如二叶式主动脉瓣等非综合征性主动脉病变，采用尺寸标准来决定何时进行干预，但尺寸标准在患有综合征性遗传性主动脉病变的患者中可能并不适用。本小型综述的目的是为遗传性主动脉病变患者的外科治疗提供总体概述和指导。
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